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Antioxidant Defense, Redox Homeostasis, and Oxidative Damage in Children With Ataxia Telangiectasia and Nijmegen Breakage Syndrome

Ataxia-telangiectasia (AT) and Nijmegen breakage syndrome (NBS) belong to a group of primary immunodeficiency diseases (PI) characterized by premature aging, cerebral degeneration, immunoglobulin deficiency and higher cancer susceptibility. Despite the fact that oxidative stress has been demonstrate...

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Detalles Bibliográficos
Autores principales:	Maciejczyk, Mateusz, Heropolitanska-Pliszka, Edyta, Pietrucha, Barbara, Sawicka-Powierza, Jolanta, Bernatowska, Ewa, Wolska-Kusnierz, Beata, Pac, Małgorzata, Car, Halina, Zalewska, Anna, Mikoluc, Bozena
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Frontiers Media S.A. 2019
Materias:	Immunology
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6776633/ https://www.ncbi.nlm.nih.gov/pubmed/31611883 http://dx.doi.org/10.3389/fimmu.2019.02322

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