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Variably protease‐sensitive prionopathy mimicking frontotemporal dementia

Sporadic prion diseases are fatal neurodegenerative disorders characterized clinically by rapidly progressive dementia and myoclonus. Variably protease‐sensitive prionopathy (VPSPr) is a recently identified sporadic human prion disorder that may present with a lengthy atypical clinical history. Here...

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Detalles Bibliográficos
Autores principales:	Aizpurua, Miren, Selvackadunco, Sashika, Yull, Helen, Kipps, Christopher M., Ironside, James W., Bodi, Istvan
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	John Wiley & Sons Australia, Ltd 2019
Materias:	Case Reports
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6778052/ https://www.ncbi.nlm.nih.gov/pubmed/30847986 http://dx.doi.org/10.1111/neup.12538

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