Pulmonary Fibrosis in Children

Pulmonary fibrosis (PF) is a very rare condition in children, which may be observed in specific forms of interstitial lung disease. None of the clinical, radiological, or histological descriptions used for PF diagnosis in adult patients, especially in situations of idiopathic PF, can apply to pediat...

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Autores principales: Nathan, Nadia, Sileo, Chiara, Thouvenin, Guillaume, Berdah, Laura, Delestrain, Céline, Manali, Effrosyne, Papiris, Spyros, Léger, Pierre-Louis, Ducou le Pointe, Hubert, Coulomb l’Hermine, Aurore, Clement, Annick
Formato: Online Artículo Texto
Lenguaje:English
Publicado: MDPI 2019
Materias:
Review
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6780823/
https://www.ncbi.nlm.nih.gov/pubmed/31455000
http://dx.doi.org/10.3390/jcm8091312
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author Nathan, Nadia
Sileo, Chiara
Thouvenin, Guillaume
Berdah, Laura
Delestrain, Céline
Manali, Effrosyne
Papiris, Spyros
Léger, Pierre-Louis
Ducou le Pointe, Hubert
Coulomb l’Hermine, Aurore
Clement, Annick
author_facet Nathan, Nadia
Sileo, Chiara
Thouvenin, Guillaume
Berdah, Laura
Delestrain, Céline
Manali, Effrosyne
Papiris, Spyros
Léger, Pierre-Louis
Ducou le Pointe, Hubert
Coulomb l’Hermine, Aurore
Clement, Annick
author_sort Nathan, Nadia
collection PubMed
description Pulmonary fibrosis (PF) is a very rare condition in children, which may be observed in specific forms of interstitial lung disease. None of the clinical, radiological, or histological descriptions used for PF diagnosis in adult patients, especially in situations of idiopathic PF, can apply to pediatric situations. This observation supports the view that PF expression may differ with age and, most likely, may cover distinct entities. The present review aims at summarizing the current understanding of PF pathophysiology in children and identifying suitable diagnostic criteria.
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spelling pubmed-67808232019-10-30 Pulmonary Fibrosis in Children Nathan, Nadia Sileo, Chiara Thouvenin, Guillaume Berdah, Laura Delestrain, Céline Manali, Effrosyne Papiris, Spyros Léger, Pierre-Louis Ducou le Pointe, Hubert Coulomb l’Hermine, Aurore Clement, Annick J Clin Med Review Pulmonary fibrosis (PF) is a very rare condition in children, which may be observed in specific forms of interstitial lung disease. None of the clinical, radiological, or histological descriptions used for PF diagnosis in adult patients, especially in situations of idiopathic PF, can apply to pediatric situations. This observation supports the view that PF expression may differ with age and, most likely, may cover distinct entities. The present review aims at summarizing the current understanding of PF pathophysiology in children and identifying suitable diagnostic criteria. MDPI 2019-08-26 /pmc/articles/PMC6780823/ /pubmed/31455000 http://dx.doi.org/10.3390/jcm8091312 Text en © 2019 by the authors. Licensee MDPI, Basel, Switzerland. This article is an open access article distributed under the terms and conditions of the Creative Commons Attribution (CC BY) license (http://creativecommons.org/licenses/by/4.0/).
spellingShingle Review
Nathan, Nadia
Sileo, Chiara
Thouvenin, Guillaume
Berdah, Laura
Delestrain, Céline
Manali, Effrosyne
Papiris, Spyros
Léger, Pierre-Louis
Ducou le Pointe, Hubert
Coulomb l’Hermine, Aurore
Clement, Annick
Pulmonary Fibrosis in Children
title Pulmonary Fibrosis in Children
title_full Pulmonary Fibrosis in Children
title_fullStr Pulmonary Fibrosis in Children
title_full_unstemmed Pulmonary Fibrosis in Children
title_short Pulmonary Fibrosis in Children
title_sort pulmonary fibrosis in children
topic Review
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6780823/
https://www.ncbi.nlm.nih.gov/pubmed/31455000
http://dx.doi.org/10.3390/jcm8091312
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