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Treatment experience of thoracic aortic aneurysm recurrence after multiple surgeries for Marfan syndrome: A case report

RATIONALE: Marfan syndrome (MFS), an autosomal dominant hereditary disease, often results in structural and functional abnormalities of the aortic wall. Because of residual aortic aneurysm or aortic dissection, patients with MFS usually need repeat operations after the first operation. PATIENT CONCE...

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Detalles Bibliográficos
Autores principales: Chen, Huai-Dong, He, Fan, Qian, Xi-Ming
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Wolters Kluwer Health 2019
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6783246/
https://www.ncbi.nlm.nih.gov/pubmed/31577745
http://dx.doi.org/10.1097/MD.0000000000017391
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author Chen, Huai-Dong
He, Fan
Qian, Xi-Ming
author_facet Chen, Huai-Dong
He, Fan
Qian, Xi-Ming
author_sort Chen, Huai-Dong
collection PubMed
description RATIONALE: Marfan syndrome (MFS), an autosomal dominant hereditary disease, often results in structural and functional abnormalities of the aortic wall. Because of residual aortic aneurysm or aortic dissection, patients with MFS usually need repeat operations after the first operation. PATIENT CONCERNS: A patient diagnosed with MFS who had undergone 2 surgeries because of abdominal aortic dissection aneurysm and Stanford A type aortic dissection at different times. DIAGNOSES: MFS. INTERVENTIONS: Due to aneurysmal dilatation of the residual descending aorta, we performed the third surgery for him through using 2 artificial stent grafts to fix and package the area of the remaining vessel in our hospital. OUTCOMES: The result was good, and the patient was discharged successfully. LESSONS: Using artificial material to repair and wrap the area of the residual vessel during the first surgery can provide an anchor area for future endovascular stent implantation and also offer a possibility for stent implantation in patients with MFS.
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spelling pubmed-67832462019-11-13 Treatment experience of thoracic aortic aneurysm recurrence after multiple surgeries for Marfan syndrome: A case report Chen, Huai-Dong He, Fan Qian, Xi-Ming Medicine (Baltimore) 3400 RATIONALE: Marfan syndrome (MFS), an autosomal dominant hereditary disease, often results in structural and functional abnormalities of the aortic wall. Because of residual aortic aneurysm or aortic dissection, patients with MFS usually need repeat operations after the first operation. PATIENT CONCERNS: A patient diagnosed with MFS who had undergone 2 surgeries because of abdominal aortic dissection aneurysm and Stanford A type aortic dissection at different times. DIAGNOSES: MFS. INTERVENTIONS: Due to aneurysmal dilatation of the residual descending aorta, we performed the third surgery for him through using 2 artificial stent grafts to fix and package the area of the remaining vessel in our hospital. OUTCOMES: The result was good, and the patient was discharged successfully. LESSONS: Using artificial material to repair and wrap the area of the residual vessel during the first surgery can provide an anchor area for future endovascular stent implantation and also offer a possibility for stent implantation in patients with MFS. Wolters Kluwer Health 2019-10-04 /pmc/articles/PMC6783246/ /pubmed/31577745 http://dx.doi.org/10.1097/MD.0000000000017391 Text en Copyright © 2019 the Author(s). Published by Wolters Kluwer Health, Inc. http://creativecommons.org/licenses/by/4.0 This is an open access article distributed under the Creative Commons Attribution License 4.0 (CCBY), which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited. http://creativecommons.org/licenses/by/4.0
spellingShingle 3400
Chen, Huai-Dong
He, Fan
Qian, Xi-Ming
Treatment experience of thoracic aortic aneurysm recurrence after multiple surgeries for Marfan syndrome: A case report
title Treatment experience of thoracic aortic aneurysm recurrence after multiple surgeries for Marfan syndrome: A case report
title_full Treatment experience of thoracic aortic aneurysm recurrence after multiple surgeries for Marfan syndrome: A case report
title_fullStr Treatment experience of thoracic aortic aneurysm recurrence after multiple surgeries for Marfan syndrome: A case report
title_full_unstemmed Treatment experience of thoracic aortic aneurysm recurrence after multiple surgeries for Marfan syndrome: A case report
title_short Treatment experience of thoracic aortic aneurysm recurrence after multiple surgeries for Marfan syndrome: A case report
title_sort treatment experience of thoracic aortic aneurysm recurrence after multiple surgeries for marfan syndrome: a case report
topic 3400
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6783246/
https://www.ncbi.nlm.nih.gov/pubmed/31577745
http://dx.doi.org/10.1097/MD.0000000000017391
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