A large epithelioid angiomyolipoma of the kidney in a very young child with idiopathic chylothorax: A diagnostic dilemma

Epithelioid angiomyolipoma (EAML) is a subtype of angiomyolipoma, the most common benign renal tumour and usually asymptomatic until adulthood. This paper reports a patient with EAML identified at 30 months, the youngest age of presentation with this tumour reported in the literature. In this case t...

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Autores principales: Kakaje, Ameer, Mujahed, Raghad, Hamdan, Othman, Hakim, Jihad
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2019
Materias:
Pediatrics
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6796615/
https://www.ncbi.nlm.nih.gov/pubmed/31641614
http://dx.doi.org/10.1016/j.eucr.2019.101035
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author Kakaje, Ameer
Mujahed, Raghad
Hamdan, Othman
Hakim, Jihad
author_facet Kakaje, Ameer
Mujahed, Raghad
Hamdan, Othman
Hakim, Jihad
author_sort Kakaje, Ameer
collection PubMed
description Epithelioid angiomyolipoma (EAML) is a subtype of angiomyolipoma, the most common benign renal tumour and usually asymptomatic until adulthood. This paper reports a patient with EAML identified at 30 months, the youngest age of presentation with this tumour reported in the literature. In this case the tumour was extremely large andwas successfully surgically removed. Furthermore, the patient had no other TS features, presented with acute symptoms, and had bilateral idiopathic chylothorax which was managed by octreotide and diet.
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spelling pubmed-67966152019-10-22 A large epithelioid angiomyolipoma of the kidney in a very young child with idiopathic chylothorax: A diagnostic dilemma Kakaje, Ameer Mujahed, Raghad Hamdan, Othman Hakim, Jihad Urol Case Rep Pediatrics Epithelioid angiomyolipoma (EAML) is a subtype of angiomyolipoma, the most common benign renal tumour and usually asymptomatic until adulthood. This paper reports a patient with EAML identified at 30 months, the youngest age of presentation with this tumour reported in the literature. In this case the tumour was extremely large andwas successfully surgically removed. Furthermore, the patient had no other TS features, presented with acute symptoms, and had bilateral idiopathic chylothorax which was managed by octreotide and diet. Elsevier 2019-10-03 /pmc/articles/PMC6796615/ /pubmed/31641614 http://dx.doi.org/10.1016/j.eucr.2019.101035 Text en © 2019 The Authors http://creativecommons.org/licenses/by-nc-nd/4.0/ This is an open access article under the CC BY-NC-ND license (http://creativecommons.org/licenses/by-nc-nd/4.0/).
spellingShingle Pediatrics
Kakaje, Ameer
Mujahed, Raghad
Hamdan, Othman
Hakim, Jihad
A large epithelioid angiomyolipoma of the kidney in a very young child with idiopathic chylothorax: A diagnostic dilemma
title A large epithelioid angiomyolipoma of the kidney in a very young child with idiopathic chylothorax: A diagnostic dilemma
title_full A large epithelioid angiomyolipoma of the kidney in a very young child with idiopathic chylothorax: A diagnostic dilemma
title_fullStr A large epithelioid angiomyolipoma of the kidney in a very young child with idiopathic chylothorax: A diagnostic dilemma
title_full_unstemmed A large epithelioid angiomyolipoma of the kidney in a very young child with idiopathic chylothorax: A diagnostic dilemma
title_short A large epithelioid angiomyolipoma of the kidney in a very young child with idiopathic chylothorax: A diagnostic dilemma
title_sort large epithelioid angiomyolipoma of the kidney in a very young child with idiopathic chylothorax: a diagnostic dilemma
topic Pediatrics
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6796615/
https://www.ncbi.nlm.nih.gov/pubmed/31641614
http://dx.doi.org/10.1016/j.eucr.2019.101035
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