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A Multidisciplinary Approach to the Management of Severe Purpura Fulminans in a Burn Center: A Case Series

Purpura fulminans is a life-threatening hematological emergency characterized by skin necrosis and disseminated intravascular coagulation requiring rapid diagnosis and treatment. We present a case series of patients with severe purpura fulminans who were managed via a multidisciplinary approach at a...

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Detalles Bibliográficos
Autores principales: Asif, Mohammed, Quiroga, Luis, Lagziel, Tomer, Ladd, Seth B, Caffrey, Julie
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Cureus 2019
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6805038/
https://www.ncbi.nlm.nih.gov/pubmed/31646137
http://dx.doi.org/10.7759/cureus.5478
Descripción
Sumario:Purpura fulminans is a life-threatening hematological emergency characterized by skin necrosis and disseminated intravascular coagulation requiring rapid diagnosis and treatment. We present a case series of patients with severe purpura fulminans who were managed via a multidisciplinary approach at a regional burn center. We report the burn unit perspective which includes current intensive care guidelines with early surgical intervention, in addition to a review of the pathology and clinical features of the disease. Proper wound management and expeditious surgical evaluation can help reduce the mortality and minimize amputations. Early referral to a burn center with a multidisciplinary team is recommended for the best outcomes in these patients.