A Case of Primary Central Nervous System Vasculitis That Worsened Despite Early Corticosteroid Therapy

Primary central nervous system vasculitis (PCNSV) is rare, and the diagnosis is difficult to make because of its variable radiologic expressions. Early corticosteroid therapy often is effective. Herein we report the case of a 56-year-old man who had a well-enhanced cystic mass with severe edema in t...

Descripción completa

Detalles Bibliográficos
Autores principales: Yoon, Sang-Youl, Park, Ki-Su, Park, Seong-Hyun, Park, Ji-Young
Formato: Online Artículo Texto
Lenguaje:English
Publicado: The Korean Brain Tumor Society; The Korean Society for Neuro-Oncology; The Korean Society for Pediatric Neuro-Oncology 2019
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6829087/
https://www.ncbi.nlm.nih.gov/pubmed/31686451
http://dx.doi.org/10.14791/btrt.2019.7.e37
Descripción
Sumario:Primary central nervous system vasculitis (PCNSV) is rare, and the diagnosis is difficult to make because of its variable radiologic expressions. Early corticosteroid therapy often is effective. Herein we report the case of a 56-year-old man who had a well-enhanced cystic mass with severe edema in the right frontal lobe, which was initially felt to be a malignancy. Histologic examination of tissue removed at craniotomy revealed that it was a PCNSV. Despite early administration of corticosteroids, a new lesion developed within 3 days. The lesions responded to treatment with cyclophosphamide and corticosteroid.

Ejemplares similares