Budd-Chiari Syndrome in a Patient With Simultaneous Diagnosis of Hepatic Sarcoidosis and Nodular Regenerative Hyperplasia

Budd-Chiari syndrome (BCS) is a rare vascular disorder characterized by an obstruction of the hepatic venous outflow. Nodular regenerative hyperplasia (NRH) may develop as a result of an underlying autoimmune disease such as hepatic sarcoidosis. Only a few case reports have described cases with eith...

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Autores principales: Odah, Tarek, Al-Khazraji, Ahmed, Idriss, Rajab, Morrow, Matthew, Curry, Michael P.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Wolters Kluwer 2019
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6831147/
https://www.ncbi.nlm.nih.gov/pubmed/31750374
http://dx.doi.org/10.14309/crj.0000000000000200
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author Odah, Tarek
Al-Khazraji, Ahmed
Idriss, Rajab
Morrow, Matthew
Curry, Michael P.
author_facet Odah, Tarek
Al-Khazraji, Ahmed
Idriss, Rajab
Morrow, Matthew
Curry, Michael P.
author_sort Odah, Tarek
collection PubMed
description Budd-Chiari syndrome (BCS) is a rare vascular disorder characterized by an obstruction of the hepatic venous outflow. Nodular regenerative hyperplasia (NRH) may develop as a result of an underlying autoimmune disease such as hepatic sarcoidosis. Only a few case reports have described cases with either NRH or hepatic sarcoidosis associated with BCS. We present a 42-year-old man presenting with BCS and signs of portal hypertension who was found to have an underlying pathological diagnosis of both hepatic sarcoidosis and NRH and who was successfully treated with a transjugular intrahepatic portosystemic shunt.
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spelling pubmed-68311472019-11-20 Budd-Chiari Syndrome in a Patient With Simultaneous Diagnosis of Hepatic Sarcoidosis and Nodular Regenerative Hyperplasia Odah, Tarek Al-Khazraji, Ahmed Idriss, Rajab Morrow, Matthew Curry, Michael P. ACG Case Rep J Case Report Budd-Chiari syndrome (BCS) is a rare vascular disorder characterized by an obstruction of the hepatic venous outflow. Nodular regenerative hyperplasia (NRH) may develop as a result of an underlying autoimmune disease such as hepatic sarcoidosis. Only a few case reports have described cases with either NRH or hepatic sarcoidosis associated with BCS. We present a 42-year-old man presenting with BCS and signs of portal hypertension who was found to have an underlying pathological diagnosis of both hepatic sarcoidosis and NRH and who was successfully treated with a transjugular intrahepatic portosystemic shunt. Wolters Kluwer 2019-09-12 /pmc/articles/PMC6831147/ /pubmed/31750374 http://dx.doi.org/10.14309/crj.0000000000000200 Text en © 2019 The Author(s). Published by Wolters Kluwer Health, Inc. on behalf of The American College of Gastroenterology. This is an open-access article distributed under the terms of the Creative Commons Attribution-Non Commercial-No Derivatives License 4.0 (CCBY-NC-ND) (http://creativecommons.org/licenses/by-nc-nd/4.0/) , where it is permissible to download and share the work provided it is properly cited. The work cannot be changed in any way or used commercially without permission from the journal.
spellingShingle Case Report
Odah, Tarek
Al-Khazraji, Ahmed
Idriss, Rajab
Morrow, Matthew
Curry, Michael P.
Budd-Chiari Syndrome in a Patient With Simultaneous Diagnosis of Hepatic Sarcoidosis and Nodular Regenerative Hyperplasia
title Budd-Chiari Syndrome in a Patient With Simultaneous Diagnosis of Hepatic Sarcoidosis and Nodular Regenerative Hyperplasia
title_full Budd-Chiari Syndrome in a Patient With Simultaneous Diagnosis of Hepatic Sarcoidosis and Nodular Regenerative Hyperplasia
title_fullStr Budd-Chiari Syndrome in a Patient With Simultaneous Diagnosis of Hepatic Sarcoidosis and Nodular Regenerative Hyperplasia
title_full_unstemmed Budd-Chiari Syndrome in a Patient With Simultaneous Diagnosis of Hepatic Sarcoidosis and Nodular Regenerative Hyperplasia
title_short Budd-Chiari Syndrome in a Patient With Simultaneous Diagnosis of Hepatic Sarcoidosis and Nodular Regenerative Hyperplasia
title_sort budd-chiari syndrome in a patient with simultaneous diagnosis of hepatic sarcoidosis and nodular regenerative hyperplasia
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6831147/
https://www.ncbi.nlm.nih.gov/pubmed/31750374
http://dx.doi.org/10.14309/crj.0000000000000200
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