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Copper extraction: Dental consideration for Wilson's disease – An uncommon case report

Wilson's disease is a very rare and inherited autosomal recessive disease of copper metabolism. The cause of the disease is mutation of the Adenosine triphosphate 7B (ATP7B gene). The ATP7B gene is responsible for biliary excretion of copper and incorporation of copper into ceruloplasmin. The i...

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Autores principales: Pandyan, Deepak A., Giri, G. V. V., Shanthi, K., Suthanraj, A. K., Kumar, Santosh
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Wolters Kluwer - Medknow 2019
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6883878/
https://www.ncbi.nlm.nih.gov/pubmed/31798263
http://dx.doi.org/10.4103/njms.NJMS_60_18
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author Pandyan, Deepak A.
Giri, G. V. V.
Shanthi, K.
Suthanraj, A. K.
Kumar, Santosh
author_facet Pandyan, Deepak A.
Giri, G. V. V.
Shanthi, K.
Suthanraj, A. K.
Kumar, Santosh
author_sort Pandyan, Deepak A.
collection PubMed
description Wilson's disease is a very rare and inherited autosomal recessive disease of copper metabolism. The cause of the disease is mutation of the Adenosine triphosphate 7B (ATP7B gene). The ATP7B gene is responsible for biliary excretion of copper and incorporation of copper into ceruloplasmin. The imbalance in the copper metabolism leads to copper toxicity which primarily involves the brain, liver, the kidney, and the skeletal system. Early diagnosis and intervention is needed to prevent the mortality and morbidity of the disease. In this article, we focus on the evaluation and dental management of patients with Wilson's disease.
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spelling pubmed-68838782019-12-03 Copper extraction: Dental consideration for Wilson's disease – An uncommon case report Pandyan, Deepak A. Giri, G. V. V. Shanthi, K. Suthanraj, A. K. Kumar, Santosh Natl J Maxillofac Surg Case Report Wilson's disease is a very rare and inherited autosomal recessive disease of copper metabolism. The cause of the disease is mutation of the Adenosine triphosphate 7B (ATP7B gene). The ATP7B gene is responsible for biliary excretion of copper and incorporation of copper into ceruloplasmin. The imbalance in the copper metabolism leads to copper toxicity which primarily involves the brain, liver, the kidney, and the skeletal system. Early diagnosis and intervention is needed to prevent the mortality and morbidity of the disease. In this article, we focus on the evaluation and dental management of patients with Wilson's disease. Wolters Kluwer - Medknow 2019 2019-11-12 /pmc/articles/PMC6883878/ /pubmed/31798263 http://dx.doi.org/10.4103/njms.NJMS_60_18 Text en Copyright: © 2019 National Journal of Maxillofacial Surgery http://creativecommons.org/licenses/by-nc-sa/4.0 This is an open access journal, and articles are distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 4.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as appropriate credit is given and the new creations are licensed under the identical terms.
spellingShingle Case Report
Pandyan, Deepak A.
Giri, G. V. V.
Shanthi, K.
Suthanraj, A. K.
Kumar, Santosh
Copper extraction: Dental consideration for Wilson's disease – An uncommon case report
title Copper extraction: Dental consideration for Wilson's disease – An uncommon case report
title_full Copper extraction: Dental consideration for Wilson's disease – An uncommon case report
title_fullStr Copper extraction: Dental consideration for Wilson's disease – An uncommon case report
title_full_unstemmed Copper extraction: Dental consideration for Wilson's disease – An uncommon case report
title_short Copper extraction: Dental consideration for Wilson's disease – An uncommon case report
title_sort copper extraction: dental consideration for wilson's disease – an uncommon case report
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6883878/
https://www.ncbi.nlm.nih.gov/pubmed/31798263
http://dx.doi.org/10.4103/njms.NJMS_60_18
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