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Goldenhar Syndrome in a 6-Year-Old Patient: a Case Report and Review of Literature

Goldenhar syndrome (GHS) is a complex syndrome characterized by relation of mandibular hypoplasia, abnormality of the ear, ocular dermoid and vertebral disorders and hemi facial macrosomia. Treatment protocol depends on the patient’s age and systemic clinical presentations, with a multidisciplinary...

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Detalles Bibliográficos
Autores principales: Jahanimoghadam, Fatemeh, Sharifi, Maryam
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Shiraz University of Medical Sciences 2019
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6890820/
https://www.ncbi.nlm.nih.gov/pubmed/31875178
http://dx.doi.org/10.30476/DENTJODS.2019.44905
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author Jahanimoghadam, Fatemeh
Sharifi, Maryam
author_facet Jahanimoghadam, Fatemeh
Sharifi, Maryam
author_sort Jahanimoghadam, Fatemeh
collection PubMed
description Goldenhar syndrome (GHS) is a complex syndrome characterized by relation of mandibular hypoplasia, abnormality of the ear, ocular dermoid and vertebral disorders and hemi facial macrosomia. Treatment protocol depends on the patient’s age and systemic clinical presentations, with a multidisciplinary method often being required. This case report describes a typical 6-year-old female patient who presented to the Department of Pediatric Dentistry, Faculty of Dentistry, University of Medical Sciences, Kerman, Iran with mandibular hypoplasia, facial asymmetry, ear tags and ocular dermoid after plastic surgery. Diagnosis was based on clinical aspects, radiology and laboratory findings. GHS is a developmental complaint that can disturb many aspects of the patient's life; therefore, immediate treatment from birth is necessary.
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spelling pubmed-68908202019-12-24 Goldenhar Syndrome in a 6-Year-Old Patient: a Case Report and Review of Literature Jahanimoghadam, Fatemeh Sharifi, Maryam J Dent (Shiraz) Case Reports Goldenhar syndrome (GHS) is a complex syndrome characterized by relation of mandibular hypoplasia, abnormality of the ear, ocular dermoid and vertebral disorders and hemi facial macrosomia. Treatment protocol depends on the patient’s age and systemic clinical presentations, with a multidisciplinary method often being required. This case report describes a typical 6-year-old female patient who presented to the Department of Pediatric Dentistry, Faculty of Dentistry, University of Medical Sciences, Kerman, Iran with mandibular hypoplasia, facial asymmetry, ear tags and ocular dermoid after plastic surgery. Diagnosis was based on clinical aspects, radiology and laboratory findings. GHS is a developmental complaint that can disturb many aspects of the patient's life; therefore, immediate treatment from birth is necessary. Shiraz University of Medical Sciences 2019-12 /pmc/articles/PMC6890820/ /pubmed/31875178 http://dx.doi.org/10.30476/DENTJODS.2019.44905 Text en Copyright: © Shiraz University of Medical Sciences http://creativecommons.org/licenses/by-nc-sa/3.0 This is an open-access article distributed under the terms of the Creative Commons Attribution-Noncommercial-Share Alike 3.0 Unported, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Reports
Jahanimoghadam, Fatemeh
Sharifi, Maryam
Goldenhar Syndrome in a 6-Year-Old Patient: a Case Report and Review of Literature
title Goldenhar Syndrome in a 6-Year-Old Patient: a Case Report and Review of Literature
title_full Goldenhar Syndrome in a 6-Year-Old Patient: a Case Report and Review of Literature
title_fullStr Goldenhar Syndrome in a 6-Year-Old Patient: a Case Report and Review of Literature
title_full_unstemmed Goldenhar Syndrome in a 6-Year-Old Patient: a Case Report and Review of Literature
title_short Goldenhar Syndrome in a 6-Year-Old Patient: a Case Report and Review of Literature
title_sort goldenhar syndrome in a 6-year-old patient: a case report and review of literature
topic Case Reports
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6890820/
https://www.ncbi.nlm.nih.gov/pubmed/31875178
http://dx.doi.org/10.30476/DENTJODS.2019.44905
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