Use of waxy maize heat modified starch in the treatment of children between 2 and 5 years with glycogen storage disease type I: A retrospective study

BACKGROUND: Glycogen storage disease type I (GSDI) is caused by deficiency of the enzyme glucose-6-phosphatase or glucose-6-phosphate transporter. Mainstay of treatment is provision of uncooked cornstarch (and/or continuous nocturnal pump feed (CNPF) to maintain normoglycemia). Waxy maize heat modif...

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Detalles Bibliográficos
Autores principales: Hijazi, Ghada, Pai, Nisha, Nagy, Laura L., Herd, Sarah, Dickson, Jolynn, Ram, Maya, Inbar-Feigenberg, Michal
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2019
Materias:
Research Paper
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6895741/
https://www.ncbi.nlm.nih.gov/pubmed/31844626
http://dx.doi.org/10.1016/j.ymgmr.2019.100536

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