Isolated unilateral pulmonary artery agenesis presenting with massive hemoptysis

This case was about a 21‐year‐old man with recurrent and persistent hemoptysis. Chest computed tomography scan showed a right‐sided pulmonary artery agenesis and associated hypertrophic change of right side bronchial arteries. Thoracic aortogram revealed abnormal collateral arteries supplying the right lung. Minor hemoptysis continued even after endovascular embolization of collateral vessels was performed. Right pneumonectomy was performed and the patient was treated successfully. Physicians should be aware that unilateral pulmonary artery agenesis could be a source of hemoptysis and pneumonectomy may be the best treatment.