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Oral health-related quality of life in Loeys-Dietz syndrome, a rare connective tissue disorder: an observational cohort study

BACKGROUND: Loeys-Dietz syndrome (LDS) is a rare connective tissue disorder whose oral manifestations and dental phenotypes have not been well-characterized. The aim of this study was to explore the influence of oral manifestations on oral health-related quality of life (OHRQoL) in LDS patients. MAT...

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Detalles Bibliográficos
Autores principales:	Nguyen, Quynh C., Duverger, Olivier, Mishra, Rashmi, Mitnik, Gabriela Lopez, Jani, Priyam, Frischmeyer-Guerrerio, Pamela A., Lee, Janice S.
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	BioMed Central 2019
Materias:	Research
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6915860/ https://www.ncbi.nlm.nih.gov/pubmed/31842932 http://dx.doi.org/10.1186/s13023-019-1250-y

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