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Late puerperal hemorrhage of a patient with Klippel–Trenaunay syndrome: A case report

INTRODUCTION: The Klippel–Trenaunay syndrome (KTS) is a rare congenital disorder. The obstetric course of women with KTS varies. Complications include bleeding, disseminated intravascular coagulation (DIC), thromboembolic events, etc. PATIENT CONCERNS: Here, we report a case of late puerperal hemorr...

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Detalles Bibliográficos
Autores principales: Zhang, Jian, Wang, Kana, Mei, Jie
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Wolters Kluwer Health 2019
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6922477/
https://www.ncbi.nlm.nih.gov/pubmed/31852150
http://dx.doi.org/10.1097/MD.0000000000018378
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author Zhang, Jian
Wang, Kana
Mei, Jie
author_facet Zhang, Jian
Wang, Kana
Mei, Jie
author_sort Zhang, Jian
collection PubMed
description INTRODUCTION: The Klippel–Trenaunay syndrome (KTS) is a rare congenital disorder. The obstetric course of women with KTS varies. Complications include bleeding, disseminated intravascular coagulation (DIC), thromboembolic events, etc. PATIENT CONCERNS: Here, we report a case of late puerperal hemorrhage of a Chinese puerpera with KTS. The repeating severe hemorrhage, the DIC, and the Kasabach–Merrit syndrome made the treatment more difficult. DIAGNOSIS: KTS is a mixed malformation with a vascular component that is characterized by abnormal development of veins, capillaries, and lymphatics. Our patient was first diagnosed with KTS at the last trimester of pregnancy. INTERVENTIONS: Massive infusion of blood products, two laparotomies, as well as bilateral internal iliac artery embolization was carried out. OUTCOMES: Although the patient survived from the life-threatening hemorrhage, she lost her uterus forever. CONCLUSION: An interdisciplinary cooperation of obstetrician, anesthesiologist, vascular surgeon, and intensive care physician is highly recommended. Prophylactic anticoagulation is generally advised in the gestational and postpartum period.
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spelling pubmed-69224772020-01-23 Late puerperal hemorrhage of a patient with Klippel–Trenaunay syndrome: A case report Zhang, Jian Wang, Kana Mei, Jie Medicine (Baltimore) 5600 INTRODUCTION: The Klippel–Trenaunay syndrome (KTS) is a rare congenital disorder. The obstetric course of women with KTS varies. Complications include bleeding, disseminated intravascular coagulation (DIC), thromboembolic events, etc. PATIENT CONCERNS: Here, we report a case of late puerperal hemorrhage of a Chinese puerpera with KTS. The repeating severe hemorrhage, the DIC, and the Kasabach–Merrit syndrome made the treatment more difficult. DIAGNOSIS: KTS is a mixed malformation with a vascular component that is characterized by abnormal development of veins, capillaries, and lymphatics. Our patient was first diagnosed with KTS at the last trimester of pregnancy. INTERVENTIONS: Massive infusion of blood products, two laparotomies, as well as bilateral internal iliac artery embolization was carried out. OUTCOMES: Although the patient survived from the life-threatening hemorrhage, she lost her uterus forever. CONCLUSION: An interdisciplinary cooperation of obstetrician, anesthesiologist, vascular surgeon, and intensive care physician is highly recommended. Prophylactic anticoagulation is generally advised in the gestational and postpartum period. Wolters Kluwer Health 2019-12-16 /pmc/articles/PMC6922477/ /pubmed/31852150 http://dx.doi.org/10.1097/MD.0000000000018378 Text en Copyright © 2019 the Author(s). Published by Wolters Kluwer Health, Inc. http://creativecommons.org/licenses/by/4.0 This is an open access article distributed under the Creative Commons Attribution License 4.0 (CCBY), which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited. http://creativecommons.org/licenses/by/4.0
spellingShingle 5600
Zhang, Jian
Wang, Kana
Mei, Jie
Late puerperal hemorrhage of a patient with Klippel–Trenaunay syndrome: A case report
title Late puerperal hemorrhage of a patient with Klippel–Trenaunay syndrome: A case report
title_full Late puerperal hemorrhage of a patient with Klippel–Trenaunay syndrome: A case report
title_fullStr Late puerperal hemorrhage of a patient with Klippel–Trenaunay syndrome: A case report
title_full_unstemmed Late puerperal hemorrhage of a patient with Klippel–Trenaunay syndrome: A case report
title_short Late puerperal hemorrhage of a patient with Klippel–Trenaunay syndrome: A case report
title_sort late puerperal hemorrhage of a patient with klippel–trenaunay syndrome: a case report
topic 5600
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6922477/
https://www.ncbi.nlm.nih.gov/pubmed/31852150
http://dx.doi.org/10.1097/MD.0000000000018378
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