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Idiopathic thrombocytopenic purpura in a patient with situs inversus totalis: case report and literature review

Situs inversus totalis is a rare recessive autosomal congenital abnormality in which the mediastinal and abdominal organs are in a mirrored position when compared to the usual topography. The literature reports some cases of situs inversus totalis and concomitant conditions: spinal abnormalities, ca...

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Autores principales: Bo, Carolina Rodrigues Dal, Devito, Beatriz Piovesana, Devito, Leticia Piovesana, del Papa, Gabriella Paes, Hamerschlak, Nelson
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Instituto Israelita de Ensino e Pesquisa Albert Einstein 2019
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6924875/
https://www.ncbi.nlm.nih.gov/pubmed/31939527
http://dx.doi.org/10.31744/einstein_journal/2020RC5111
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author Bo, Carolina Rodrigues Dal
Devito, Beatriz Piovesana
Devito, Leticia Piovesana
del Papa, Gabriella Paes
Hamerschlak, Nelson
author_facet Bo, Carolina Rodrigues Dal
Devito, Beatriz Piovesana
Devito, Leticia Piovesana
del Papa, Gabriella Paes
Hamerschlak, Nelson
author_sort Bo, Carolina Rodrigues Dal
collection PubMed
description Situs inversus totalis is a rare recessive autosomal congenital abnormality in which the mediastinal and abdominal organs are in a mirrored position when compared to the usual topography. The literature reports some cases of situs inversus totalis and concomitant conditions: spinal abnormalities, cardiac malformations and hematological diseases, such as idiopathic thrombocytopenic purpura, which is an autoimmune disease that causes thrombocytopenia due to platelet destruction or suppression of its production. This article aimed to report the coexistence of situs inversus totalis and idiopathic thrombocytopenic purpura.
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spelling pubmed-69248752020-01-31 Idiopathic thrombocytopenic purpura in a patient with situs inversus totalis: case report and literature review Bo, Carolina Rodrigues Dal Devito, Beatriz Piovesana Devito, Leticia Piovesana del Papa, Gabriella Paes Hamerschlak, Nelson Einstein (Sao Paulo) Case Report Situs inversus totalis is a rare recessive autosomal congenital abnormality in which the mediastinal and abdominal organs are in a mirrored position when compared to the usual topography. The literature reports some cases of situs inversus totalis and concomitant conditions: spinal abnormalities, cardiac malformations and hematological diseases, such as idiopathic thrombocytopenic purpura, which is an autoimmune disease that causes thrombocytopenia due to platelet destruction or suppression of its production. This article aimed to report the coexistence of situs inversus totalis and idiopathic thrombocytopenic purpura. Instituto Israelita de Ensino e Pesquisa Albert Einstein 2019-12-20 /pmc/articles/PMC6924875/ /pubmed/31939527 http://dx.doi.org/10.31744/einstein_journal/2020RC5111 Text en http://creativecommons.org/licenses/by/4.0/ This content is licensed under a Creative Commons Attribution 4.0 International License.
spellingShingle Case Report
Bo, Carolina Rodrigues Dal
Devito, Beatriz Piovesana
Devito, Leticia Piovesana
del Papa, Gabriella Paes
Hamerschlak, Nelson
Idiopathic thrombocytopenic purpura in a patient with situs inversus totalis: case report and literature review
title Idiopathic thrombocytopenic purpura in a patient with situs inversus totalis: case report and literature review
title_full Idiopathic thrombocytopenic purpura in a patient with situs inversus totalis: case report and literature review
title_fullStr Idiopathic thrombocytopenic purpura in a patient with situs inversus totalis: case report and literature review
title_full_unstemmed Idiopathic thrombocytopenic purpura in a patient with situs inversus totalis: case report and literature review
title_short Idiopathic thrombocytopenic purpura in a patient with situs inversus totalis: case report and literature review
title_sort idiopathic thrombocytopenic purpura in a patient with situs inversus totalis: case report and literature review
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6924875/
https://www.ncbi.nlm.nih.gov/pubmed/31939527
http://dx.doi.org/10.31744/einstein_journal/2020RC5111
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