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Hirayama’s Disease in a Young Male: A Rare Case Report

Hirayama disease is a rare neurological condition also known as monomelic amyotrophy (MMA). It is a type of cervical myelopathy, which involves the anterior horn cells and affects the distal upper extremities. It is self-limited, asymmetrical lower motor weakness of hands and forearms. Young males a...

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Detalles Bibliográficos
Autores principales: Kumar, Mukesh, Athwal, Pal Satyajit Singh, Rhandhawa, Sandeep, Kahlon, Sukhmanii, Shiv Kumar, Jeevan
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Cureus 2019
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6925375/
https://www.ncbi.nlm.nih.gov/pubmed/31890406
http://dx.doi.org/10.7759/cureus.6204
Descripción
Sumario:Hirayama disease is a rare neurological condition also known as monomelic amyotrophy (MMA). It is a type of cervical myelopathy, which involves the anterior horn cells and affects the distal upper extremities. It is self-limited, asymmetrical lower motor weakness of hands and forearms. Young males are more commonly affected. The condition is hypothesized to occur due to an asymmetric compression of the cervical spinal cord by the dural sac, however, the exact mechanism(s) continue to be investigated. We report a case of a 20-year-old male who presented with complaints of right hand and forearm weakness, who was diagnosed with Hirayama disease and treated.