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Hirayama’s Disease in a Young Male: A Rare Case Report

Hirayama disease is a rare neurological condition also known as monomelic amyotrophy (MMA). It is a type of cervical myelopathy, which involves the anterior horn cells and affects the distal upper extremities. It is self-limited, asymmetrical lower motor weakness of hands and forearms. Young males a...

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Autores principales: Kumar, Mukesh, Athwal, Pal Satyajit Singh, Rhandhawa, Sandeep, Kahlon, Sukhmanii, Shiv Kumar, Jeevan
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Cureus 2019
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6925375/
https://www.ncbi.nlm.nih.gov/pubmed/31890406
http://dx.doi.org/10.7759/cureus.6204
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author Kumar, Mukesh
Athwal, Pal Satyajit Singh
Rhandhawa, Sandeep
Kahlon, Sukhmanii
Shiv Kumar, Jeevan
author_facet Kumar, Mukesh
Athwal, Pal Satyajit Singh
Rhandhawa, Sandeep
Kahlon, Sukhmanii
Shiv Kumar, Jeevan
author_sort Kumar, Mukesh
collection PubMed
description Hirayama disease is a rare neurological condition also known as monomelic amyotrophy (MMA). It is a type of cervical myelopathy, which involves the anterior horn cells and affects the distal upper extremities. It is self-limited, asymmetrical lower motor weakness of hands and forearms. Young males are more commonly affected. The condition is hypothesized to occur due to an asymmetric compression of the cervical spinal cord by the dural sac, however, the exact mechanism(s) continue to be investigated. We report a case of a 20-year-old male who presented with complaints of right hand and forearm weakness, who was diagnosed with Hirayama disease and treated.
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spelling pubmed-69253752019-12-30 Hirayama’s Disease in a Young Male: A Rare Case Report Kumar, Mukesh Athwal, Pal Satyajit Singh Rhandhawa, Sandeep Kahlon, Sukhmanii Shiv Kumar, Jeevan Cureus Neurology Hirayama disease is a rare neurological condition also known as monomelic amyotrophy (MMA). It is a type of cervical myelopathy, which involves the anterior horn cells and affects the distal upper extremities. It is self-limited, asymmetrical lower motor weakness of hands and forearms. Young males are more commonly affected. The condition is hypothesized to occur due to an asymmetric compression of the cervical spinal cord by the dural sac, however, the exact mechanism(s) continue to be investigated. We report a case of a 20-year-old male who presented with complaints of right hand and forearm weakness, who was diagnosed with Hirayama disease and treated. Cureus 2019-11-19 /pmc/articles/PMC6925375/ /pubmed/31890406 http://dx.doi.org/10.7759/cureus.6204 Text en Copyright © 2019, Kumar et al. http://creativecommons.org/licenses/by/3.0/ This is an open access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.
spellingShingle Neurology
Kumar, Mukesh
Athwal, Pal Satyajit Singh
Rhandhawa, Sandeep
Kahlon, Sukhmanii
Shiv Kumar, Jeevan
Hirayama’s Disease in a Young Male: A Rare Case Report
title Hirayama’s Disease in a Young Male: A Rare Case Report
title_full Hirayama’s Disease in a Young Male: A Rare Case Report
title_fullStr Hirayama’s Disease in a Young Male: A Rare Case Report
title_full_unstemmed Hirayama’s Disease in a Young Male: A Rare Case Report
title_short Hirayama’s Disease in a Young Male: A Rare Case Report
title_sort hirayama’s disease in a young male: a rare case report
topic Neurology
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6925375/
https://www.ncbi.nlm.nih.gov/pubmed/31890406
http://dx.doi.org/10.7759/cureus.6204
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