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Rare Mesenteric Arterial Diseases: Fibromuscular Dysplasia and Segmental Arterial Mediolysis and Literature Review

Fibromuscular dysplasia (FMD) and segmental arterial mediolysis (SAM) are noninflammatory, nonatherosclerotic arterial diseases that cause aneurysm, occlusion, and thromboses. These diseases are rarely seen in mesenteric arterial lesions; however, as they can be lethal if appropriate management is n...

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Autores principales: Ko, Masayoshi, Kamimura, Kenya, Sakamaki, Akira, Niwa, Yusuke, Tominaga, Kentaro, Mizuno, Kenichi, Terai, Shuji
Formato: Online Artículo Texto
Lenguaje:English
Publicado: The Japanese Society of Internal Medicine 2019
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6928505/
https://www.ncbi.nlm.nih.gov/pubmed/31327836
http://dx.doi.org/10.2169/internalmedicine.3094-19
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author Ko, Masayoshi
Kamimura, Kenya
Sakamaki, Akira
Niwa, Yusuke
Tominaga, Kentaro
Mizuno, Kenichi
Terai, Shuji
author_facet Ko, Masayoshi
Kamimura, Kenya
Sakamaki, Akira
Niwa, Yusuke
Tominaga, Kentaro
Mizuno, Kenichi
Terai, Shuji
author_sort Ko, Masayoshi
collection PubMed
description Fibromuscular dysplasia (FMD) and segmental arterial mediolysis (SAM) are noninflammatory, nonatherosclerotic arterial diseases that cause aneurysm, occlusion, and thromboses. These diseases are rarely seen in mesenteric arterial lesions; however, as they can be lethal if appropriate management is not provided, the accumulation of clinical information from cases is essential. We herein report the cases of a 57-year-old man diagnosed with FMD and a 63-year-old man diagnosed with SAM. We conclude that an early diagnosis with imaging modalities and clinical information followed by the appropriate treatment improves the prognosis of these arterial diseases.
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spelling pubmed-69285052019-12-26 Rare Mesenteric Arterial Diseases: Fibromuscular Dysplasia and Segmental Arterial Mediolysis and Literature Review Ko, Masayoshi Kamimura, Kenya Sakamaki, Akira Niwa, Yusuke Tominaga, Kentaro Mizuno, Kenichi Terai, Shuji Intern Med Case Report Fibromuscular dysplasia (FMD) and segmental arterial mediolysis (SAM) are noninflammatory, nonatherosclerotic arterial diseases that cause aneurysm, occlusion, and thromboses. These diseases are rarely seen in mesenteric arterial lesions; however, as they can be lethal if appropriate management is not provided, the accumulation of clinical information from cases is essential. We herein report the cases of a 57-year-old man diagnosed with FMD and a 63-year-old man diagnosed with SAM. We conclude that an early diagnosis with imaging modalities and clinical information followed by the appropriate treatment improves the prognosis of these arterial diseases. The Japanese Society of Internal Medicine 2019-07-22 2019-12-01 /pmc/articles/PMC6928505/ /pubmed/31327836 http://dx.doi.org/10.2169/internalmedicine.3094-19 Text en Copyright © 2019 by The Japanese Society of Internal Medicine https://creativecommons.org/licenses/by-nc-nd/4.0/ The Internal Medicine is an Open Access journal distributed under the Creative Commons Attribution-NonCommercial-NoDerivatives 4.0 International License. To view the details of this license, please visit (https://creativecommons.org/licenses/by-nc-nd/4.0/).
spellingShingle Case Report
Ko, Masayoshi
Kamimura, Kenya
Sakamaki, Akira
Niwa, Yusuke
Tominaga, Kentaro
Mizuno, Kenichi
Terai, Shuji
Rare Mesenteric Arterial Diseases: Fibromuscular Dysplasia and Segmental Arterial Mediolysis and Literature Review
title Rare Mesenteric Arterial Diseases: Fibromuscular Dysplasia and Segmental Arterial Mediolysis and Literature Review
title_full Rare Mesenteric Arterial Diseases: Fibromuscular Dysplasia and Segmental Arterial Mediolysis and Literature Review
title_fullStr Rare Mesenteric Arterial Diseases: Fibromuscular Dysplasia and Segmental Arterial Mediolysis and Literature Review
title_full_unstemmed Rare Mesenteric Arterial Diseases: Fibromuscular Dysplasia and Segmental Arterial Mediolysis and Literature Review
title_short Rare Mesenteric Arterial Diseases: Fibromuscular Dysplasia and Segmental Arterial Mediolysis and Literature Review
title_sort rare mesenteric arterial diseases: fibromuscular dysplasia and segmental arterial mediolysis and literature review
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6928505/
https://www.ncbi.nlm.nih.gov/pubmed/31327836
http://dx.doi.org/10.2169/internalmedicine.3094-19
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