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Rare Mesenteric Arterial Diseases: Fibromuscular Dysplasia and Segmental Arterial Mediolysis and Literature Review
Fibromuscular dysplasia (FMD) and segmental arterial mediolysis (SAM) are noninflammatory, nonatherosclerotic arterial diseases that cause aneurysm, occlusion, and thromboses. These diseases are rarely seen in mesenteric arterial lesions; however, as they can be lethal if appropriate management is n...
Autores principales: | , , , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
The Japanese Society of Internal Medicine
2019
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6928505/ https://www.ncbi.nlm.nih.gov/pubmed/31327836 http://dx.doi.org/10.2169/internalmedicine.3094-19 |
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author | Ko, Masayoshi Kamimura, Kenya Sakamaki, Akira Niwa, Yusuke Tominaga, Kentaro Mizuno, Kenichi Terai, Shuji |
author_facet | Ko, Masayoshi Kamimura, Kenya Sakamaki, Akira Niwa, Yusuke Tominaga, Kentaro Mizuno, Kenichi Terai, Shuji |
author_sort | Ko, Masayoshi |
collection | PubMed |
description | Fibromuscular dysplasia (FMD) and segmental arterial mediolysis (SAM) are noninflammatory, nonatherosclerotic arterial diseases that cause aneurysm, occlusion, and thromboses. These diseases are rarely seen in mesenteric arterial lesions; however, as they can be lethal if appropriate management is not provided, the accumulation of clinical information from cases is essential. We herein report the cases of a 57-year-old man diagnosed with FMD and a 63-year-old man diagnosed with SAM. We conclude that an early diagnosis with imaging modalities and clinical information followed by the appropriate treatment improves the prognosis of these arterial diseases. |
format | Online Article Text |
id | pubmed-6928505 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2019 |
publisher | The Japanese Society of Internal Medicine |
record_format | MEDLINE/PubMed |
spelling | pubmed-69285052019-12-26 Rare Mesenteric Arterial Diseases: Fibromuscular Dysplasia and Segmental Arterial Mediolysis and Literature Review Ko, Masayoshi Kamimura, Kenya Sakamaki, Akira Niwa, Yusuke Tominaga, Kentaro Mizuno, Kenichi Terai, Shuji Intern Med Case Report Fibromuscular dysplasia (FMD) and segmental arterial mediolysis (SAM) are noninflammatory, nonatherosclerotic arterial diseases that cause aneurysm, occlusion, and thromboses. These diseases are rarely seen in mesenteric arterial lesions; however, as they can be lethal if appropriate management is not provided, the accumulation of clinical information from cases is essential. We herein report the cases of a 57-year-old man diagnosed with FMD and a 63-year-old man diagnosed with SAM. We conclude that an early diagnosis with imaging modalities and clinical information followed by the appropriate treatment improves the prognosis of these arterial diseases. The Japanese Society of Internal Medicine 2019-07-22 2019-12-01 /pmc/articles/PMC6928505/ /pubmed/31327836 http://dx.doi.org/10.2169/internalmedicine.3094-19 Text en Copyright © 2019 by The Japanese Society of Internal Medicine https://creativecommons.org/licenses/by-nc-nd/4.0/ The Internal Medicine is an Open Access journal distributed under the Creative Commons Attribution-NonCommercial-NoDerivatives 4.0 International License. To view the details of this license, please visit (https://creativecommons.org/licenses/by-nc-nd/4.0/). |
spellingShingle | Case Report Ko, Masayoshi Kamimura, Kenya Sakamaki, Akira Niwa, Yusuke Tominaga, Kentaro Mizuno, Kenichi Terai, Shuji Rare Mesenteric Arterial Diseases: Fibromuscular Dysplasia and Segmental Arterial Mediolysis and Literature Review |
title | Rare Mesenteric Arterial Diseases: Fibromuscular Dysplasia and Segmental Arterial Mediolysis and Literature Review |
title_full | Rare Mesenteric Arterial Diseases: Fibromuscular Dysplasia and Segmental Arterial Mediolysis and Literature Review |
title_fullStr | Rare Mesenteric Arterial Diseases: Fibromuscular Dysplasia and Segmental Arterial Mediolysis and Literature Review |
title_full_unstemmed | Rare Mesenteric Arterial Diseases: Fibromuscular Dysplasia and Segmental Arterial Mediolysis and Literature Review |
title_short | Rare Mesenteric Arterial Diseases: Fibromuscular Dysplasia and Segmental Arterial Mediolysis and Literature Review |
title_sort | rare mesenteric arterial diseases: fibromuscular dysplasia and segmental arterial mediolysis and literature review |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6928505/ https://www.ncbi.nlm.nih.gov/pubmed/31327836 http://dx.doi.org/10.2169/internalmedicine.3094-19 |
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