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Suspected pleuroparenchymal fibroelastosis relapse after lung transplantation: a case report and literature review
Pleuroparenchymal fibroelastosis (PPFE) is a very rare lung disease characterized by dense fibrous thickening of the visceral pleura and intraalveolar fibrosis containing prominent elastosis, with typical upper lobe predominance. PPFE usually shows progressive restrictive ventilatory impairment refr...
Autores principales: | Rasciti, Edoardo, Cancellieri, Alessandra, Romagnoli, Micaela, Dell'Amore, Andrea, Zompatori, Maurizio |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
The British Institute of Radiology.
2019
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6945250/ https://www.ncbi.nlm.nih.gov/pubmed/31938568 http://dx.doi.org/10.1259/bjrcr.20190040 |
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