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Primary Immunodeficiency with Severe Multi-Organ Immune Dysregulation

Polyglandular autoimmune syndrome type 1, also known as autoimmune polyendocrinopathy-candidiasis-ectodermal dystrophy (APECED), is a rare primary immunodeficiency disorder with multi-organ involvement. Besides for being predisposed to severe life-threatening infections, patients with APECED are als...

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Detalles Bibliográficos
Autor principal:	Gavrilova, Tatyana
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Hindawi 2019
Materias:	Case Report
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6949663/ https://www.ncbi.nlm.nih.gov/pubmed/31956453 http://dx.doi.org/10.1155/2019/8746249

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