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Maxillary mesenchymal chondrosarcoma leading to a diagnosis of Li-Fraumeni syndrome

Mesenchymal chondrosarcoma (MCS) is a rare histological variant of chondrosarcoma, with aggressive behaviour. Due to the unique nature of this disease, management strategies are not well established. Li-Fraumeni syndrome (LFS) is a rare cancer predisposition syndrome with a wide tumour spectrum, ass...

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Detalles Bibliográficos
Autores principales:	Ventura, Eduardo, Dionísio, Sílvia, Ferreira, Ângela, Saleiro, Rute, Marques, Hugo, Magalhães, Manuel, Monteiro, Carlos
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Oxford University Press 2020
Materias:	Case Report
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6963167/ https://www.ncbi.nlm.nih.gov/pubmed/31976063 http://dx.doi.org/10.1093/jscr/rjz386

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