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Difficult airway associated with bifid glottis and coexistent subglottic stenosis in a patient with Pallister–Hall syndrome: a case report

BACKGROUND: Pallister–Hall syndrome is a rare disorder characterized by hypothalamic hamartoma, hypopituitarism, bifid epiglottis, and micrognathia. CASE PRESENTATION: We describe the airway management under general anesthesia of a 15-year-old female with Pallister–Hall syndrome whose airway was com...

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Autores principales: Oe, Yukimura, Godai, Kohei, Masuda, Mina, Kanmura, Yuichi
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Springer Berlin Heidelberg 2018
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6966929/
https://www.ncbi.nlm.nih.gov/pubmed/32025855
http://dx.doi.org/10.1186/s40981-018-0158-1
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author Oe, Yukimura
Godai, Kohei
Masuda, Mina
Kanmura, Yuichi
author_facet Oe, Yukimura
Godai, Kohei
Masuda, Mina
Kanmura, Yuichi
author_sort Oe, Yukimura
collection PubMed
description BACKGROUND: Pallister–Hall syndrome is a rare disorder characterized by hypothalamic hamartoma, hypopituitarism, bifid epiglottis, and micrognathia. CASE PRESENTATION: We describe the airway management under general anesthesia of a 15-year-old female with Pallister–Hall syndrome whose airway was compromised with bifid epiglottis and acquired subglottic stenosis. The three options considered for airway management were tracheal intubation, a supraglottic device, and surgical tracheotomy. Tracheal intubation provides a secured airway, but extubation can be difficult. A supraglottic device minimizes airway injury, but it does not completely protect the airway from aspiration. CONCLUSIONS: The patient’s airway was successfully managed using a supraglottic device with aspiration prophylaxis. Airway management devices should be selected according to each patients’ individual circumstances. ELECTRONIC SUPPLEMENTARY MATERIAL: The online version of this article (10.1186/s40981-018-0158-1) contains supplementary material, which is available to authorized users.
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spelling pubmed-69669292020-02-04 Difficult airway associated with bifid glottis and coexistent subglottic stenosis in a patient with Pallister–Hall syndrome: a case report Oe, Yukimura Godai, Kohei Masuda, Mina Kanmura, Yuichi JA Clin Rep Case Report BACKGROUND: Pallister–Hall syndrome is a rare disorder characterized by hypothalamic hamartoma, hypopituitarism, bifid epiglottis, and micrognathia. CASE PRESENTATION: We describe the airway management under general anesthesia of a 15-year-old female with Pallister–Hall syndrome whose airway was compromised with bifid epiglottis and acquired subglottic stenosis. The three options considered for airway management were tracheal intubation, a supraglottic device, and surgical tracheotomy. Tracheal intubation provides a secured airway, but extubation can be difficult. A supraglottic device minimizes airway injury, but it does not completely protect the airway from aspiration. CONCLUSIONS: The patient’s airway was successfully managed using a supraglottic device with aspiration prophylaxis. Airway management devices should be selected according to each patients’ individual circumstances. ELECTRONIC SUPPLEMENTARY MATERIAL: The online version of this article (10.1186/s40981-018-0158-1) contains supplementary material, which is available to authorized users. Springer Berlin Heidelberg 2018-02-23 /pmc/articles/PMC6966929/ /pubmed/32025855 http://dx.doi.org/10.1186/s40981-018-0158-1 Text en © The Author(s) 2018 Open Access This article is distributed under the terms of the Creative Commons Attribution 4.0 International License (http://creativecommons.org/licenses/by/4.0/), which permits unrestricted use, distribution, and reproduction in any medium, provided you give appropriate credit to the original author(s) and the source, provide a link to the Creative Commons license, and indicate if changes were made.
spellingShingle Case Report
Oe, Yukimura
Godai, Kohei
Masuda, Mina
Kanmura, Yuichi
Difficult airway associated with bifid glottis and coexistent subglottic stenosis in a patient with Pallister–Hall syndrome: a case report
title Difficult airway associated with bifid glottis and coexistent subglottic stenosis in a patient with Pallister–Hall syndrome: a case report
title_full Difficult airway associated with bifid glottis and coexistent subglottic stenosis in a patient with Pallister–Hall syndrome: a case report
title_fullStr Difficult airway associated with bifid glottis and coexistent subglottic stenosis in a patient with Pallister–Hall syndrome: a case report
title_full_unstemmed Difficult airway associated with bifid glottis and coexistent subglottic stenosis in a patient with Pallister–Hall syndrome: a case report
title_short Difficult airway associated with bifid glottis and coexistent subglottic stenosis in a patient with Pallister–Hall syndrome: a case report
title_sort difficult airway associated with bifid glottis and coexistent subglottic stenosis in a patient with pallister–hall syndrome: a case report
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6966929/
https://www.ncbi.nlm.nih.gov/pubmed/32025855
http://dx.doi.org/10.1186/s40981-018-0158-1
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