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The Extrapulmonary Effects of Cystic Fibrosis Transmembrane Conductance Regulator Modulators in Cystic Fibrosis

The effects of cystic fibrosis (CF) transmembrane conductance regulator (CFTR) modulators on lung function, pulmonary exacerbations, and quality of life have been well documented. However, CF is a multiorgan disease, and therefore an evidence base is emerging on the systemic effects of CFTR modulato...

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Detalles Bibliográficos
Autores principales:	Sergeev, Valentine, Chou, Frank Y., Lam, Grace Y., Hamilton, Christopher Michael, Wilcox, Pearce G., Quon, Bradley S.
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	American Thoracic Society 2020
Materias:	Focused Reviews
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6993798/ https://www.ncbi.nlm.nih.gov/pubmed/31661636 http://dx.doi.org/10.1513/AnnalsATS.201909-671CME

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