Cargando…
Parry–Romberg syndrome in an adolescent: a case report on progressive hemifacial atrophy
Parry–Romberg syndrome is a rare degenerative disorder causing progressive atrophy of skin and soft tissues of the face and neck, which is usually unilateral. The mean age of onset is usually in the second decade of life and the disease causes functional, aesthetic and psychological disabilities in...
Autores principales: | , |
---|---|
Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Oxford University Press
2020
|
Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6996043/ https://www.ncbi.nlm.nih.gov/pubmed/32038874 http://dx.doi.org/10.1093/omcr/omz127 |
_version_ | 1783493459568492544 |
---|---|
author | Srinivasan, Ranjini Joy, Shasta Theresa |
author_facet | Srinivasan, Ranjini Joy, Shasta Theresa |
author_sort | Srinivasan, Ranjini |
collection | PubMed |
description | Parry–Romberg syndrome is a rare degenerative disorder causing progressive atrophy of skin and soft tissues of the face and neck, which is usually unilateral. The mean age of onset is usually in the second decade of life and the disease causes functional, aesthetic and psychological disabilities in the affected individual. We present a 14-year-old boy with this disorder. The diagnosis was based on clinical characteristics. A multidisciplinary team approach involving rheumatologists, dermatologists, maxillofacial surgeons, dentists and psychologists is required for the management of this problem, which is mainly targeted at controlling active inflammation with the use of immunosuppressive agents in addition to possible surgical correction of repositioning of adipose tissue that is lost due to atrophy. |
format | Online Article Text |
id | pubmed-6996043 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2020 |
publisher | Oxford University Press |
record_format | MEDLINE/PubMed |
spelling | pubmed-69960432020-02-07 Parry–Romberg syndrome in an adolescent: a case report on progressive hemifacial atrophy Srinivasan, Ranjini Joy, Shasta Theresa Oxf Med Case Reports Case Report Parry–Romberg syndrome is a rare degenerative disorder causing progressive atrophy of skin and soft tissues of the face and neck, which is usually unilateral. The mean age of onset is usually in the second decade of life and the disease causes functional, aesthetic and psychological disabilities in the affected individual. We present a 14-year-old boy with this disorder. The diagnosis was based on clinical characteristics. A multidisciplinary team approach involving rheumatologists, dermatologists, maxillofacial surgeons, dentists and psychologists is required for the management of this problem, which is mainly targeted at controlling active inflammation with the use of immunosuppressive agents in addition to possible surgical correction of repositioning of adipose tissue that is lost due to atrophy. Oxford University Press 2020-01-31 /pmc/articles/PMC6996043/ /pubmed/32038874 http://dx.doi.org/10.1093/omcr/omz127 Text en © The Author(s) 2020. Published by Oxford University Press. http://creativecommons.org/licenses/by-nc/4.0/ This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/4.0/), which permits non-commercial re-use, distribution, and reproduction in any medium, provided the original work is properly cited. For commercial re-use, please contact journals.permissions@oup.com |
spellingShingle | Case Report Srinivasan, Ranjini Joy, Shasta Theresa Parry–Romberg syndrome in an adolescent: a case report on progressive hemifacial atrophy |
title | Parry–Romberg syndrome in an adolescent: a case report on progressive hemifacial atrophy |
title_full | Parry–Romberg syndrome in an adolescent: a case report on progressive hemifacial atrophy |
title_fullStr | Parry–Romberg syndrome in an adolescent: a case report on progressive hemifacial atrophy |
title_full_unstemmed | Parry–Romberg syndrome in an adolescent: a case report on progressive hemifacial atrophy |
title_short | Parry–Romberg syndrome in an adolescent: a case report on progressive hemifacial atrophy |
title_sort | parry–romberg syndrome in an adolescent: a case report on progressive hemifacial atrophy |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6996043/ https://www.ncbi.nlm.nih.gov/pubmed/32038874 http://dx.doi.org/10.1093/omcr/omz127 |
work_keys_str_mv | AT srinivasanranjini parryrombergsyndromeinanadolescentacasereportonprogressivehemifacialatrophy AT joyshastatheresa parryrombergsyndromeinanadolescentacasereportonprogressivehemifacialatrophy |