Spontaneous rupture of large bilateral renal angiomyolipomas in a patient with tuberous sclerosis complex: A case report and literature review

Enormous bilateral renal angiomyolipoma (AML) are extremely rare, their spontaneous bleeding also called Wunderlich's syndrom (WS) is also an unusual situation. It is considered as a life threatening condition requiring fast and effective care. We present a case of hypovolemic shock due to spon...

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Detalles Bibliográficos
Autores principales: Ben Mansoura, Wissem, Ben Rhouma, Sami, Jrad, Myriam, Zehani, Alia, Boukriba, Seifeddine, Mizouni, Habiba
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2020
Materias:
Oncology
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6997209/
https://www.ncbi.nlm.nih.gov/pubmed/32025496
http://dx.doi.org/10.1016/j.eucr.2020.101124
Descripción
Sumario:Enormous bilateral renal angiomyolipoma (AML) are extremely rare, their spontaneous bleeding also called Wunderlich's syndrom (WS) is also an unusual situation. It is considered as a life threatening condition requiring fast and effective care. We present a case of hypovolemic shock due to spontaneous rupture of bilateral giant angiomyolipomas in a 35-year-old female patient with tuberous sclerosis complex (TSC). The hemodynamic instability of the patient leads to an immediate surgery and unilateral nephrectomy was done for the biggest angiomyolipomas. The review of the literature revealed only few cases of spontaneous rupture of renal angiomyolipomas of comparable size.

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