Spontaneous rupture of large bilateral renal angiomyolipomas in a patient with tuberous sclerosis complex: A case report and literature review

Enormous bilateral renal angiomyolipoma (AML) are extremely rare, their spontaneous bleeding also called Wunderlich's syndrom (WS) is also an unusual situation. It is considered as a life threatening condition requiring fast and effective care. We present a case of hypovolemic shock due to spon...

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Autores principales: Ben Mansoura, Wissem, Ben Rhouma, Sami, Jrad, Myriam, Zehani, Alia, Boukriba, Seifeddine, Mizouni, Habiba
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2020
Materias:
Oncology
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6997209/
https://www.ncbi.nlm.nih.gov/pubmed/32025496
http://dx.doi.org/10.1016/j.eucr.2020.101124
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author Ben Mansoura, Wissem
Ben Rhouma, Sami
Jrad, Myriam
Zehani, Alia
Boukriba, Seifeddine
Mizouni, Habiba
author_facet Ben Mansoura, Wissem
Ben Rhouma, Sami
Jrad, Myriam
Zehani, Alia
Boukriba, Seifeddine
Mizouni, Habiba
author_sort Ben Mansoura, Wissem
collection PubMed
description Enormous bilateral renal angiomyolipoma (AML) are extremely rare, their spontaneous bleeding also called Wunderlich's syndrom (WS) is also an unusual situation. It is considered as a life threatening condition requiring fast and effective care. We present a case of hypovolemic shock due to spontaneous rupture of bilateral giant angiomyolipomas in a 35-year-old female patient with tuberous sclerosis complex (TSC). The hemodynamic instability of the patient leads to an immediate surgery and unilateral nephrectomy was done for the biggest angiomyolipomas. The review of the literature revealed only few cases of spontaneous rupture of renal angiomyolipomas of comparable size.
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spelling pubmed-69972092020-02-05 Spontaneous rupture of large bilateral renal angiomyolipomas in a patient with tuberous sclerosis complex: A case report and literature review Ben Mansoura, Wissem Ben Rhouma, Sami Jrad, Myriam Zehani, Alia Boukriba, Seifeddine Mizouni, Habiba Urol Case Rep Oncology Enormous bilateral renal angiomyolipoma (AML) are extremely rare, their spontaneous bleeding also called Wunderlich's syndrom (WS) is also an unusual situation. It is considered as a life threatening condition requiring fast and effective care. We present a case of hypovolemic shock due to spontaneous rupture of bilateral giant angiomyolipomas in a 35-year-old female patient with tuberous sclerosis complex (TSC). The hemodynamic instability of the patient leads to an immediate surgery and unilateral nephrectomy was done for the biggest angiomyolipomas. The review of the literature revealed only few cases of spontaneous rupture of renal angiomyolipomas of comparable size. Elsevier 2020-01-22 /pmc/articles/PMC6997209/ /pubmed/32025496 http://dx.doi.org/10.1016/j.eucr.2020.101124 Text en © 2020 Published by Elsevier Inc. http://creativecommons.org/licenses/by-nc-nd/4.0/ This is an open access article under the CC BY-NC-ND license (http://creativecommons.org/licenses/by-nc-nd/4.0/).
spellingShingle Oncology
Ben Mansoura, Wissem
Ben Rhouma, Sami
Jrad, Myriam
Zehani, Alia
Boukriba, Seifeddine
Mizouni, Habiba
Spontaneous rupture of large bilateral renal angiomyolipomas in a patient with tuberous sclerosis complex: A case report and literature review
title Spontaneous rupture of large bilateral renal angiomyolipomas in a patient with tuberous sclerosis complex: A case report and literature review
title_full Spontaneous rupture of large bilateral renal angiomyolipomas in a patient with tuberous sclerosis complex: A case report and literature review
title_fullStr Spontaneous rupture of large bilateral renal angiomyolipomas in a patient with tuberous sclerosis complex: A case report and literature review
title_full_unstemmed Spontaneous rupture of large bilateral renal angiomyolipomas in a patient with tuberous sclerosis complex: A case report and literature review
title_short Spontaneous rupture of large bilateral renal angiomyolipomas in a patient with tuberous sclerosis complex: A case report and literature review
title_sort spontaneous rupture of large bilateral renal angiomyolipomas in a patient with tuberous sclerosis complex: a case report and literature review
topic Oncology
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC6997209/
https://www.ncbi.nlm.nih.gov/pubmed/32025496
http://dx.doi.org/10.1016/j.eucr.2020.101124
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