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Up-regulation of Toll-like receptors 7 and 9 and its potential implications in the pathogenic mechanisms of LMNA-related myopathies
Laminopathies are a heterogeneous group of diseases, caused by mutations in lamin A/C proteins. The most common laminopathy (LMNA-related myopathies, LMNA-RM) affects skeletal and cardiac muscles; muscle histopathology is variable, ranging from mild unspecific changes to dystrophic features, sometim...
Autores principales: | Cappelletti, Cristina, Salerno, Franco, Canioni, Eleonora, Mora, Marina, Mantegazza, Renato, Bernasconi, Pia, Maggi, Lorenzo |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Taylor & Francis
2018
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7000140/ https://www.ncbi.nlm.nih.gov/pubmed/29895224 http://dx.doi.org/10.1080/19491034.2018.1471947 |
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