A 23-Year-Old Man with Hyper-IgM Syndrome Presenting with Asymptomatic Violaceous Facial Plaques

Tumid lupus is a rare subtype of chronic cutaneous lupus that is characterized by urticaria-like photosensitive plaques. Unlike discoid lupus, it has minimal to no surface change and resolves without scarring. On pathological examination, it may be distinguished from other types of lupus by abundant...

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Detalles Bibliográficos
Autores principales: Barrios, Mirelys, Nathan, Neera, Trowbridge, Ryan, Plovanich, Molly, Nazarian, Rosalynn M., Kroshinsky, Daniela
Formato: Online Artículo Texto
Lenguaje:English
Publicado: S. Karger AG 2020
Materias:
Clinico-Pathological Correlation in Dermatopathology
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7011746/
https://www.ncbi.nlm.nih.gov/pubmed/32083062
http://dx.doi.org/10.1159/000503744
Descripción
Sumario:Tumid lupus is a rare subtype of chronic cutaneous lupus that is characterized by urticaria-like photosensitive plaques. Unlike discoid lupus, it has minimal to no surface change and resolves without scarring. On pathological examination, it may be distinguished from other types of lupus by abundant interstitial mucin deposits. Herein, we describe a case of tumid lupus in a 23-year-old Kuwaiti male with hyper-IgM syndrome. To our best knowledge, this is the first report of tumid lupus in a patient with a primary immunodeficiency.

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