Cargando…

A 23-Year-Old Man with Hyper-IgM Syndrome Presenting with Asymptomatic Violaceous Facial Plaques

Tumid lupus is a rare subtype of chronic cutaneous lupus that is characterized by urticaria-like photosensitive plaques. Unlike discoid lupus, it has minimal to no surface change and resolves without scarring. On pathological examination, it may be distinguished from other types of lupus by abundant...

Descripción completa

Detalles Bibliográficos
Autores principales: Barrios, Mirelys, Nathan, Neera, Trowbridge, Ryan, Plovanich, Molly, Nazarian, Rosalynn M., Kroshinsky, Daniela
Formato: Online Artículo Texto
Lenguaje:English
Publicado: S. Karger AG 2020
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7011746/
https://www.ncbi.nlm.nih.gov/pubmed/32083062
http://dx.doi.org/10.1159/000503744
_version_ 1783496122218577920
author Barrios, Mirelys
Nathan, Neera
Trowbridge, Ryan
Plovanich, Molly
Nazarian, Rosalynn M.
Kroshinsky, Daniela
author_facet Barrios, Mirelys
Nathan, Neera
Trowbridge, Ryan
Plovanich, Molly
Nazarian, Rosalynn M.
Kroshinsky, Daniela
author_sort Barrios, Mirelys
collection PubMed
description Tumid lupus is a rare subtype of chronic cutaneous lupus that is characterized by urticaria-like photosensitive plaques. Unlike discoid lupus, it has minimal to no surface change and resolves without scarring. On pathological examination, it may be distinguished from other types of lupus by abundant interstitial mucin deposits. Herein, we describe a case of tumid lupus in a 23-year-old Kuwaiti male with hyper-IgM syndrome. To our best knowledge, this is the first report of tumid lupus in a patient with a primary immunodeficiency.
format Online
Article
Text
id pubmed-7011746
institution National Center for Biotechnology Information
language English
publishDate 2020
publisher S. Karger AG
record_format MEDLINE/PubMed
spelling pubmed-70117462020-02-20 A 23-Year-Old Man with Hyper-IgM Syndrome Presenting with Asymptomatic Violaceous Facial Plaques Barrios, Mirelys Nathan, Neera Trowbridge, Ryan Plovanich, Molly Nazarian, Rosalynn M. Kroshinsky, Daniela Dermatopathology (Basel) Clinico-Pathological Correlation in Dermatopathology Tumid lupus is a rare subtype of chronic cutaneous lupus that is characterized by urticaria-like photosensitive plaques. Unlike discoid lupus, it has minimal to no surface change and resolves without scarring. On pathological examination, it may be distinguished from other types of lupus by abundant interstitial mucin deposits. Herein, we describe a case of tumid lupus in a 23-year-old Kuwaiti male with hyper-IgM syndrome. To our best knowledge, this is the first report of tumid lupus in a patient with a primary immunodeficiency. S. Karger AG 2020-01-22 /pmc/articles/PMC7011746/ /pubmed/32083062 http://dx.doi.org/10.1159/000503744 Text en Copyright © 2020 by S. Karger AG, Basel http://creativecommons.org/licenses/by-nc/4.0/ This article is licensed under the Creative Commons Attribution-NonCommercial-NoDerivatives 4.0 International License (CC BY-NC-ND) (http://www.karger.com/Services/OpenAccessLicense). Usage and distribution for commercial purposes requires written permission.
spellingShingle Clinico-Pathological Correlation in Dermatopathology
Barrios, Mirelys
Nathan, Neera
Trowbridge, Ryan
Plovanich, Molly
Nazarian, Rosalynn M.
Kroshinsky, Daniela
A 23-Year-Old Man with Hyper-IgM Syndrome Presenting with Asymptomatic Violaceous Facial Plaques
title A 23-Year-Old Man with Hyper-IgM Syndrome Presenting with Asymptomatic Violaceous Facial Plaques
title_full A 23-Year-Old Man with Hyper-IgM Syndrome Presenting with Asymptomatic Violaceous Facial Plaques
title_fullStr A 23-Year-Old Man with Hyper-IgM Syndrome Presenting with Asymptomatic Violaceous Facial Plaques
title_full_unstemmed A 23-Year-Old Man with Hyper-IgM Syndrome Presenting with Asymptomatic Violaceous Facial Plaques
title_short A 23-Year-Old Man with Hyper-IgM Syndrome Presenting with Asymptomatic Violaceous Facial Plaques
title_sort 23-year-old man with hyper-igm syndrome presenting with asymptomatic violaceous facial plaques
topic Clinico-Pathological Correlation in Dermatopathology
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7011746/
https://www.ncbi.nlm.nih.gov/pubmed/32083062
http://dx.doi.org/10.1159/000503744
work_keys_str_mv AT barriosmirelys a23yearoldmanwithhyperigmsyndromepresentingwithasymptomaticviolaceousfacialplaques
AT nathanneera a23yearoldmanwithhyperigmsyndromepresentingwithasymptomaticviolaceousfacialplaques
AT trowbridgeryan a23yearoldmanwithhyperigmsyndromepresentingwithasymptomaticviolaceousfacialplaques
AT plovanichmolly a23yearoldmanwithhyperigmsyndromepresentingwithasymptomaticviolaceousfacialplaques
AT nazarianrosalynnm a23yearoldmanwithhyperigmsyndromepresentingwithasymptomaticviolaceousfacialplaques
AT kroshinskydaniela a23yearoldmanwithhyperigmsyndromepresentingwithasymptomaticviolaceousfacialplaques
AT barriosmirelys 23yearoldmanwithhyperigmsyndromepresentingwithasymptomaticviolaceousfacialplaques
AT nathanneera 23yearoldmanwithhyperigmsyndromepresentingwithasymptomaticviolaceousfacialplaques
AT trowbridgeryan 23yearoldmanwithhyperigmsyndromepresentingwithasymptomaticviolaceousfacialplaques
AT plovanichmolly 23yearoldmanwithhyperigmsyndromepresentingwithasymptomaticviolaceousfacialplaques
AT nazarianrosalynnm 23yearoldmanwithhyperigmsyndromepresentingwithasymptomaticviolaceousfacialplaques
AT kroshinskydaniela 23yearoldmanwithhyperigmsyndromepresentingwithasymptomaticviolaceousfacialplaques