The use of sodium DL-3-Hydroxybutyrate in severe acute neuro-metabolic compromise in patients with inherited ketone body synthetic disorders

BACKGROUND: Ketone bodies form a vital energy source for end organs in a variety of physiological circumstances. At different times, the heart, brain and skeletal muscle in particular can use ketones as a primary substrate. Failure to generate ketones in such circumstances leads to compromised energ...

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Detalles Bibliográficos
Autores principales: Bhattacharya, Kaustuv, Matar, Walid, Tolun, Adviye Ayper, Devanapalli, Beena, Thompson, Sue, Dalkeith, Troy, Lichkus, Kate, Tchan, Michel
Formato: Online Artículo Texto
Lenguaje:English
Publicado: BioMed Central 2020
Materias:
Research
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7029565/
https://www.ncbi.nlm.nih.gov/pubmed/32070364
http://dx.doi.org/10.1186/s13023-020-1316-x

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7029565/
https://www.ncbi.nlm.nih.gov/pubmed/32070364
http://dx.doi.org/10.1186/s13023-020-1316-x

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