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Hemophagocytic lymphohistiocytosis resulting from a cytokine storm triggered by septicemia in a child with chronic granuloma disease: a case report and literature review

BACKGROUND: Hemophagocytic lymphohistiocytosis (HLH) is a rare potentially fatal illness characterized by impaired natural killer and cytotoxic T cell function. Chronic granulomatous disease (CGD) is an inherited immune deficiency caused by a defect in the nicotinamide adenine dinucleotide phosphate...

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Detalles Bibliográficos
Autores principales: Wei, Ang, Ma, Honghao, Zhang, Liping, Li, Zhigang, Zhang, Qing, Wang, Dong, Zhang, Li, Lian, Hongyun, Zhang, Rui, Wang, Tianyou
Formato: Online Artículo Texto
Lenguaje:English
Publicado: BioMed Central 2020
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7053071/
https://www.ncbi.nlm.nih.gov/pubmed/32126983
http://dx.doi.org/10.1186/s12887-020-1996-3

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