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Familial “benign” pemphigus? Erythroderma and fatal outcome()()

Hailey–Hailey disease, or familial benign pemphigus, is a rare bullous genodermatosis that usually presents with flaccid blisters, erosions, and maceration limited to flexural areas, resulting in increased morbidity and reduced quality of life for affected patients. The authors report an unusual cas...

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Detalles Bibliográficos
Autores principales: Tansini, Paula Baldissera, Boff, Ana Letícia, Weber, Magda Blessmann, Bonamigo, Renan Rangel
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Sociedade Brasileira de Dermatologia 2020
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7058835/
https://www.ncbi.nlm.nih.gov/pubmed/31959512
http://dx.doi.org/10.1016/j.abd.2019.02.006
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author Tansini, Paula Baldissera
Boff, Ana Letícia
Weber, Magda Blessmann
Bonamigo, Renan Rangel
author_facet Tansini, Paula Baldissera
Boff, Ana Letícia
Weber, Magda Blessmann
Bonamigo, Renan Rangel
author_sort Tansini, Paula Baldissera
collection PubMed
description Hailey–Hailey disease, or familial benign pemphigus, is a rare bullous genodermatosis that usually presents with flaccid blisters, erosions, and maceration limited to flexural areas, resulting in increased morbidity and reduced quality of life for affected patients. The authors report an unusual case of generalized Hailey–Hailey disease with erythroderma and fatal outcome.
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spelling pubmed-70588352020-03-11 Familial “benign” pemphigus? Erythroderma and fatal outcome()() Tansini, Paula Baldissera Boff, Ana Letícia Weber, Magda Blessmann Bonamigo, Renan Rangel An Bras Dermatol Case Report Hailey–Hailey disease, or familial benign pemphigus, is a rare bullous genodermatosis that usually presents with flaccid blisters, erosions, and maceration limited to flexural areas, resulting in increased morbidity and reduced quality of life for affected patients. The authors report an unusual case of generalized Hailey–Hailey disease with erythroderma and fatal outcome. Sociedade Brasileira de Dermatologia 2020 2019-11-25 /pmc/articles/PMC7058835/ /pubmed/31959512 http://dx.doi.org/10.1016/j.abd.2019.02.006 Text en © 2020 Sociedade Brasileira de Dermatologia. Published by Elsevier España, S.L.U. http://creativecommons.org/licenses/by/4.0/ This is an open access article under the CC BY license (http://creativecommons.org/licenses/by/4.0/).
spellingShingle Case Report
Tansini, Paula Baldissera
Boff, Ana Letícia
Weber, Magda Blessmann
Bonamigo, Renan Rangel
Familial “benign” pemphigus? Erythroderma and fatal outcome()()
title Familial “benign” pemphigus? Erythroderma and fatal outcome()()
title_full Familial “benign” pemphigus? Erythroderma and fatal outcome()()
title_fullStr Familial “benign” pemphigus? Erythroderma and fatal outcome()()
title_full_unstemmed Familial “benign” pemphigus? Erythroderma and fatal outcome()()
title_short Familial “benign” pemphigus? Erythroderma and fatal outcome()()
title_sort familial “benign” pemphigus? erythroderma and fatal outcome()()
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7058835/
https://www.ncbi.nlm.nih.gov/pubmed/31959512
http://dx.doi.org/10.1016/j.abd.2019.02.006
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