Erdheim-Chester Disease With Extensive Pericardial Involvement: A Case Report and Systematic Review

Erdheim-Chester disease (ECD) is a rare non-Langerhans cell histiocytosis characterized by systemic xanthogranulomatous infiltration. We described the case of a female adult presenting with pericardial effusion. Pericardial infiltration is the most frequent cardiac manifestation of ECD and is the on...

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Detalles Bibliográficos
Autores principales: Sanchez-Nadales, Alejandro, Anampa-Guzman, Andrea, Navarro-Motta, Jessica
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elmer Press 2020
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7092773/
https://www.ncbi.nlm.nih.gov/pubmed/32256919
http://dx.doi.org/10.14740/cr1025
Descripción
Sumario:Erdheim-Chester disease (ECD) is a rare non-Langerhans cell histiocytosis characterized by systemic xanthogranulomatous infiltration. We described the case of a female adult presenting with pericardial effusion. Pericardial infiltration is the most frequent cardiac manifestation of ECD and is the one discussed in this article. We found that the majority of patients with pericardial infiltration needed a cardiovascular procedure.

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