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AMPK Complex Activation Promotes Sarcolemmal Repair in Dysferlinopathy
Mutations in dysferlin are responsible for a group of progressive, recessively inherited muscular dystrophies known as dysferlinopathies. Using recombinant proteins and affinity purification methods combined with liquid chromatography-tandem mass spectrometry (LC-MS/MS), we found that AMP-activated...
Autores principales: | Ono, Hiroya, Suzuki, Naoki, Kanno, Shin-ichiro, Kawahara, Genri, Izumi, Rumiko, Takahashi, Toshiaki, Kitajima, Yasuo, Osana, Shion, Nakamura, Naoko, Akiyama, Tetsuya, Ikeda, Kensuke, Shijo, Tomomi, Mitsuzawa, Shio, Nagatomi, Ryoichi, Araki, Nobukazu, Yasui, Akira, Warita, Hitoshi, Hayashi, Yukiko K., Miyake, Katsuya, Aoki, Masashi |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
American Society of Gene & Cell Therapy
2020
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7132631/ https://www.ncbi.nlm.nih.gov/pubmed/32087766 http://dx.doi.org/10.1016/j.ymthe.2020.02.006 |
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