Antioxidants Reduce Muscular Dystrophy in the dy(2J)/dy(2J) Mouse Model of Laminin α2 Chain-Deficient Muscular Dystrophy

Congenital muscular dystrophy with laminin α2 chain-deficiency (LAMA2-CMD) is a severe neuromuscular disorder without a cure. Using transcriptome and proteome profiling as well as functional assays, we previously demonstrated significant metabolic impairment in skeletal muscle from LAMA2-CMD patient...

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Detalles Bibliográficos
Autores principales: Harandi, Vahid M., Moreira Soares Oliveira, Bernardo, Allamand, Valérie, Friberg, Ariana, Fontes-Oliveira, Cibely C., Durbeej, Madeleine
Formato: Online Artículo Texto
Lenguaje:English
Publicado: MDPI 2020
Materias:
Article
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7139799/
https://www.ncbi.nlm.nih.gov/pubmed/32197453
http://dx.doi.org/10.3390/antiox9030244

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7139799/
https://www.ncbi.nlm.nih.gov/pubmed/32197453
http://dx.doi.org/10.3390/antiox9030244

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