Cargando…
Natural history of lung function in spinal muscular atrophy
BACKGROUND: Respiratory muscle weakness is an important feature of spinal muscular atrophy (SMA). Progressive lung function decline is the most important cause of mortality and morbidity in patients. The natural history of lung function in SMA has, however, not been studied in much detail. RESULTS:...
Autores principales: | Wijngaarde, Camiel A., Veldhoen, Esther S., van Eijk, Ruben P. A., Stam, Marloes, Otto, Louise A. M., Asselman, Fay-Lynn, Wösten-van Asperen, Roelie M., Hulzebos, Erik H. J., Verweij-van den Oudenrijn, Laura P., Bartels, Bart, Cuppen, Inge, Wadman, Renske I., van den Berg, Leonard H., van der Ent, Cornelis K., van der Pol, W. Ludo |
---|---|
Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
BioMed Central
2020
|
Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7149916/ https://www.ncbi.nlm.nih.gov/pubmed/32276635 http://dx.doi.org/10.1186/s13023-020-01367-y |
Ejemplares similares
-
Natural history of respiratory muscle strength in spinal muscular atrophy: a prospective national cohort study
por: Veldhoen, Esther S., et al.
Publicado: (2022) -
Lung function decline preceding chronic respiratory failure in spinal muscular atrophy: a national prospective cohort study
por: Veldhoen, Esther S., et al.
Publicado: (2023) -
Relative hyperventilation in non-ventilated patients with spinal muscular atrophy
por: Veldhoen, Esther S., et al.
Publicado: (2020) -
Oscillometry: A substitute of spirometry in children with neuromuscular diseases?
por: Veldhoen, Esther S., et al.
Publicado: (2022) -
Short-term effect of air stacking and mechanical insufflation–exsufflation on lung function in patients with neuromuscular diseases
por: Veldhoen, Esther S, et al.
Publicado: (2022)