Lung Transplantation in a Patient with COPA Syndrome

COPA syndrome is a newly discovered, rare genetic autoimmune disorder, which can affect the lungs, joints, and kidneys. It is difficult to recognize, and the survival benefit of lung transplantation for these patients is not yet known. We present a case of a 24-year-old woman who received bilateral...

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Detalles Bibliográficos
Autores principales: Mallea, Jorge M., Kornafeld, Anna, Khoor, Andras, Erasmus, David B.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Hindawi 2020
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7152970/
https://www.ncbi.nlm.nih.gov/pubmed/32309005
http://dx.doi.org/10.1155/2020/3624795
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author Mallea, Jorge M.
Kornafeld, Anna
Khoor, Andras
Erasmus, David B.
author_facet Mallea, Jorge M.
Kornafeld, Anna
Khoor, Andras
Erasmus, David B.
author_sort Mallea, Jorge M.
collection PubMed
description COPA syndrome is a newly discovered, rare genetic autoimmune disorder, which can affect the lungs, joints, and kidneys. It is difficult to recognize, and the survival benefit of lung transplantation for these patients is not yet known. We present a case of a 24-year-old woman who received bilateral lung transplant for COPA syndrome. At 15 months posttransplant, her pulmonary function is stable with no episodes of acute cellular- or antibody-mediated rejection and no evidence of disease recurrence.
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spelling pubmed-71529702020-04-17 Lung Transplantation in a Patient with COPA Syndrome Mallea, Jorge M. Kornafeld, Anna Khoor, Andras Erasmus, David B. Case Rep Transplant Case Report COPA syndrome is a newly discovered, rare genetic autoimmune disorder, which can affect the lungs, joints, and kidneys. It is difficult to recognize, and the survival benefit of lung transplantation for these patients is not yet known. We present a case of a 24-year-old woman who received bilateral lung transplant for COPA syndrome. At 15 months posttransplant, her pulmonary function is stable with no episodes of acute cellular- or antibody-mediated rejection and no evidence of disease recurrence. Hindawi 2020-03-31 /pmc/articles/PMC7152970/ /pubmed/32309005 http://dx.doi.org/10.1155/2020/3624795 Text en Copyright © 2020 Jorge M. Mallea et al. http://creativecommons.org/licenses/by/4.0/ This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Mallea, Jorge M.
Kornafeld, Anna
Khoor, Andras
Erasmus, David B.
Lung Transplantation in a Patient with COPA Syndrome
title Lung Transplantation in a Patient with COPA Syndrome
title_full Lung Transplantation in a Patient with COPA Syndrome
title_fullStr Lung Transplantation in a Patient with COPA Syndrome
title_full_unstemmed Lung Transplantation in a Patient with COPA Syndrome
title_short Lung Transplantation in a Patient with COPA Syndrome
title_sort lung transplantation in a patient with copa syndrome
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7152970/
https://www.ncbi.nlm.nih.gov/pubmed/32309005
http://dx.doi.org/10.1155/2020/3624795
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