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Exacerbations and Pseudomonas aeruginosa colonization are associated with altered lung structure and function in primary ciliary dyskinesia
BACKGROUND: Recurrent bacterial infections of the respiratory tract are one of the major clinical features of the primary ciliary dyskinesia (PCD), a rare genetic disease due to malfunctioning of motile cilia. Chronic infections and persistent inflammation of the respiratory system result in progres...
Autores principales: | Piatti, G., De Santi, M. M., Farolfi, A., Zuccotti, G. V., D’Auria, E., Patria, M. F., Torretta, S., Consonni, D., Ambrosetti, U. |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
BioMed Central
2020
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7153224/ https://www.ncbi.nlm.nih.gov/pubmed/32284045 http://dx.doi.org/10.1186/s12887-020-02062-4 |
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