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Predominant dendriform pulmonary ossification in a usual interstitial pneumonia-like distribution: to be distinguished from idiopathic pulmonary fibrosis
Idiopathic dendriform diffuse pulmonary ossification (DPO) is a rare disorder. High resolution CT (HRCT) with appropriate osteoporosis window setting reveals the diagnosis. We report the features of eight patients, of whom two brothers, with HRCT findings compatible with predominant DPO in a bibasal...
Autores principales: | , , , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Mattioli 1885
2017
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7170096/ https://www.ncbi.nlm.nih.gov/pubmed/32476853 http://dx.doi.org/10.36141/svdld.v34i3.6032 |
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author | Slabbynck, Hans de Beukelaar, Tom De Surgeloose, Didier Van Goethem, Jozef Charels, Karina Bedert, Lieven Wuyts, Wim |
author_facet | Slabbynck, Hans de Beukelaar, Tom De Surgeloose, Didier Van Goethem, Jozef Charels, Karina Bedert, Lieven Wuyts, Wim |
author_sort | Slabbynck, Hans |
collection | PubMed |
description | Idiopathic dendriform diffuse pulmonary ossification (DPO) is a rare disorder. High resolution CT (HRCT) with appropriate osteoporosis window setting reveals the diagnosis. We report the features of eight patients, of whom two brothers, with HRCT findings compatible with predominant DPO in a bibasal subpleural distribution (usual interstitial pneumonia (UIP)-like distribution) and review the literature for DPO in this UIP-like distribution. DPO in a UIP-like distribution seems to be a disorder of the very old (age 75-87 (mean 83.6) male (8 out of 8), with familial occurrence, with associated cardiovascular disease and frequent use of anticoagulants as common findings, and with a slowly progressive nature and the absence of radiological honeycombing despite long lasting disease contrasting with idiopathic pulmonary fibrosis (IPF). Idiopathic pulmonary fibrosis (IPF) should be differentiated from predominant DPO in a UIP-like distibution. (Sarcoidosis Vasc Diffuse Lung Dis 2017; 34: 251-256) |
format | Online Article Text |
id | pubmed-7170096 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2017 |
publisher | Mattioli 1885 |
record_format | MEDLINE/PubMed |
spelling | pubmed-71700962020-05-29 Predominant dendriform pulmonary ossification in a usual interstitial pneumonia-like distribution: to be distinguished from idiopathic pulmonary fibrosis Slabbynck, Hans de Beukelaar, Tom De Surgeloose, Didier Van Goethem, Jozef Charels, Karina Bedert, Lieven Wuyts, Wim Sarcoidosis Vasc Diffuse Lung Dis Case Series Idiopathic dendriform diffuse pulmonary ossification (DPO) is a rare disorder. High resolution CT (HRCT) with appropriate osteoporosis window setting reveals the diagnosis. We report the features of eight patients, of whom two brothers, with HRCT findings compatible with predominant DPO in a bibasal subpleural distribution (usual interstitial pneumonia (UIP)-like distribution) and review the literature for DPO in this UIP-like distribution. DPO in a UIP-like distribution seems to be a disorder of the very old (age 75-87 (mean 83.6) male (8 out of 8), with familial occurrence, with associated cardiovascular disease and frequent use of anticoagulants as common findings, and with a slowly progressive nature and the absence of radiological honeycombing despite long lasting disease contrasting with idiopathic pulmonary fibrosis (IPF). Idiopathic pulmonary fibrosis (IPF) should be differentiated from predominant DPO in a UIP-like distibution. (Sarcoidosis Vasc Diffuse Lung Dis 2017; 34: 251-256) Mattioli 1885 2017 2017-09-30 /pmc/articles/PMC7170096/ /pubmed/32476853 http://dx.doi.org/10.36141/svdld.v34i3.6032 Text en Copyright: © 2017 http://creativecommons.org/licenses/by-nc-sa/4.0 This work is licensed under a Creative Commons Attribution 4.0 International License |
spellingShingle | Case Series Slabbynck, Hans de Beukelaar, Tom De Surgeloose, Didier Van Goethem, Jozef Charels, Karina Bedert, Lieven Wuyts, Wim Predominant dendriform pulmonary ossification in a usual interstitial pneumonia-like distribution: to be distinguished from idiopathic pulmonary fibrosis |
title | Predominant dendriform pulmonary ossification in a usual interstitial pneumonia-like distribution: to be distinguished from idiopathic pulmonary fibrosis |
title_full | Predominant dendriform pulmonary ossification in a usual interstitial pneumonia-like distribution: to be distinguished from idiopathic pulmonary fibrosis |
title_fullStr | Predominant dendriform pulmonary ossification in a usual interstitial pneumonia-like distribution: to be distinguished from idiopathic pulmonary fibrosis |
title_full_unstemmed | Predominant dendriform pulmonary ossification in a usual interstitial pneumonia-like distribution: to be distinguished from idiopathic pulmonary fibrosis |
title_short | Predominant dendriform pulmonary ossification in a usual interstitial pneumonia-like distribution: to be distinguished from idiopathic pulmonary fibrosis |
title_sort | predominant dendriform pulmonary ossification in a usual interstitial pneumonia-like distribution: to be distinguished from idiopathic pulmonary fibrosis |
topic | Case Series |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7170096/ https://www.ncbi.nlm.nih.gov/pubmed/32476853 http://dx.doi.org/10.36141/svdld.v34i3.6032 |
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