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Congenital Hepatic Fibrosis in Children and Adults: Clinical Manifestations, Management, and Outcome—Case Series and Literature Review

BACKGROUND: Congenital hepatic fibrosis is a hereditary fibropolycystic disease caused by ductal plate malformation. It is characterized by portal hypertension, but the manifestations, management, and outcome vary in children and adults. To raise awareness of medical staff, we have comprehensively c...

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Detalles Bibliográficos
Autores principales:	Zhu, Beidi, Du, Zunguo, Wang, Zhengxin, Li, Yang, Zhang, Jiming, Zhu, Haoxiang
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Hindawi 2020
Materias:	Research Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7191434/ https://www.ncbi.nlm.nih.gov/pubmed/32382272 http://dx.doi.org/10.1155/2020/8284274

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