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Giant Thrombosis at Left Anterior Descending Artery Aneurysm in a 10-Year Old Boy with Granulomatosis with Polyangiitis
Granulomatosis with polyangiitis (GPA), necrotizing vasculitis of small and medium-sized vessels, is traditionally believed to mainly affect respiratory tract with additional focal kidney involvements as its primary manifestations with a relatively rare annual incidence rate of 20-50 cases per milli...
Autores principales: | , , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Hindawi
2020
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7193272/ https://www.ncbi.nlm.nih.gov/pubmed/32373370 http://dx.doi.org/10.1155/2020/3417910 |
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author | Aghaei Moghadam, Ehsan Aslani, Nahid Mojtabavi, Helia Larti, Farnoosh Ghamari, Azin Ziaee, Vahid |
author_facet | Aghaei Moghadam, Ehsan Aslani, Nahid Mojtabavi, Helia Larti, Farnoosh Ghamari, Azin Ziaee, Vahid |
author_sort | Aghaei Moghadam, Ehsan |
collection | PubMed |
description | Granulomatosis with polyangiitis (GPA), necrotizing vasculitis of small and medium-sized vessels, is traditionally believed to mainly affect respiratory tract with additional focal kidney involvements as its primary manifestations with a relatively rare annual incidence rate of 20-50 cases per million. Six percent of the affected cases have cardiac involvements; among which, aneurysms comprise the lowest penetrance. By this paper, we aim to cast light on clinical diagnostic and treatment methods of a rare case presentation, a 10-year-old male GPA patient, diagnosed with massive thrombosis at his coronary artery aneurysm. GPA should be considered as differential diagnosis of prolong fever and coronary aneurysms in adolescents. |
format | Online Article Text |
id | pubmed-7193272 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2020 |
publisher | Hindawi |
record_format | MEDLINE/PubMed |
spelling | pubmed-71932722020-05-05 Giant Thrombosis at Left Anterior Descending Artery Aneurysm in a 10-Year Old Boy with Granulomatosis with Polyangiitis Aghaei Moghadam, Ehsan Aslani, Nahid Mojtabavi, Helia Larti, Farnoosh Ghamari, Azin Ziaee, Vahid Case Rep Cardiol Case Report Granulomatosis with polyangiitis (GPA), necrotizing vasculitis of small and medium-sized vessels, is traditionally believed to mainly affect respiratory tract with additional focal kidney involvements as its primary manifestations with a relatively rare annual incidence rate of 20-50 cases per million. Six percent of the affected cases have cardiac involvements; among which, aneurysms comprise the lowest penetrance. By this paper, we aim to cast light on clinical diagnostic and treatment methods of a rare case presentation, a 10-year-old male GPA patient, diagnosed with massive thrombosis at his coronary artery aneurysm. GPA should be considered as differential diagnosis of prolong fever and coronary aneurysms in adolescents. Hindawi 2020-04-19 /pmc/articles/PMC7193272/ /pubmed/32373370 http://dx.doi.org/10.1155/2020/3417910 Text en Copyright © 2020 Ehsan Aghaei Moghadam et al. http://creativecommons.org/licenses/by/4.0/ This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited. |
spellingShingle | Case Report Aghaei Moghadam, Ehsan Aslani, Nahid Mojtabavi, Helia Larti, Farnoosh Ghamari, Azin Ziaee, Vahid Giant Thrombosis at Left Anterior Descending Artery Aneurysm in a 10-Year Old Boy with Granulomatosis with Polyangiitis |
title | Giant Thrombosis at Left Anterior Descending Artery Aneurysm in a 10-Year Old Boy with Granulomatosis with Polyangiitis |
title_full | Giant Thrombosis at Left Anterior Descending Artery Aneurysm in a 10-Year Old Boy with Granulomatosis with Polyangiitis |
title_fullStr | Giant Thrombosis at Left Anterior Descending Artery Aneurysm in a 10-Year Old Boy with Granulomatosis with Polyangiitis |
title_full_unstemmed | Giant Thrombosis at Left Anterior Descending Artery Aneurysm in a 10-Year Old Boy with Granulomatosis with Polyangiitis |
title_short | Giant Thrombosis at Left Anterior Descending Artery Aneurysm in a 10-Year Old Boy with Granulomatosis with Polyangiitis |
title_sort | giant thrombosis at left anterior descending artery aneurysm in a 10-year old boy with granulomatosis with polyangiitis |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7193272/ https://www.ncbi.nlm.nih.gov/pubmed/32373370 http://dx.doi.org/10.1155/2020/3417910 |
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