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Giant Thrombosis at Left Anterior Descending Artery Aneurysm in a 10-Year Old Boy with Granulomatosis with Polyangiitis

Granulomatosis with polyangiitis (GPA), necrotizing vasculitis of small and medium-sized vessels, is traditionally believed to mainly affect respiratory tract with additional focal kidney involvements as its primary manifestations with a relatively rare annual incidence rate of 20-50 cases per milli...

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Autores principales: Aghaei Moghadam, Ehsan, Aslani, Nahid, Mojtabavi, Helia, Larti, Farnoosh, Ghamari, Azin, Ziaee, Vahid
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Hindawi 2020
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7193272/
https://www.ncbi.nlm.nih.gov/pubmed/32373370
http://dx.doi.org/10.1155/2020/3417910
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author Aghaei Moghadam, Ehsan
Aslani, Nahid
Mojtabavi, Helia
Larti, Farnoosh
Ghamari, Azin
Ziaee, Vahid
author_facet Aghaei Moghadam, Ehsan
Aslani, Nahid
Mojtabavi, Helia
Larti, Farnoosh
Ghamari, Azin
Ziaee, Vahid
author_sort Aghaei Moghadam, Ehsan
collection PubMed
description Granulomatosis with polyangiitis (GPA), necrotizing vasculitis of small and medium-sized vessels, is traditionally believed to mainly affect respiratory tract with additional focal kidney involvements as its primary manifestations with a relatively rare annual incidence rate of 20-50 cases per million. Six percent of the affected cases have cardiac involvements; among which, aneurysms comprise the lowest penetrance. By this paper, we aim to cast light on clinical diagnostic and treatment methods of a rare case presentation, a 10-year-old male GPA patient, diagnosed with massive thrombosis at his coronary artery aneurysm. GPA should be considered as differential diagnosis of prolong fever and coronary aneurysms in adolescents.
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spelling pubmed-71932722020-05-05 Giant Thrombosis at Left Anterior Descending Artery Aneurysm in a 10-Year Old Boy with Granulomatosis with Polyangiitis Aghaei Moghadam, Ehsan Aslani, Nahid Mojtabavi, Helia Larti, Farnoosh Ghamari, Azin Ziaee, Vahid Case Rep Cardiol Case Report Granulomatosis with polyangiitis (GPA), necrotizing vasculitis of small and medium-sized vessels, is traditionally believed to mainly affect respiratory tract with additional focal kidney involvements as its primary manifestations with a relatively rare annual incidence rate of 20-50 cases per million. Six percent of the affected cases have cardiac involvements; among which, aneurysms comprise the lowest penetrance. By this paper, we aim to cast light on clinical diagnostic and treatment methods of a rare case presentation, a 10-year-old male GPA patient, diagnosed with massive thrombosis at his coronary artery aneurysm. GPA should be considered as differential diagnosis of prolong fever and coronary aneurysms in adolescents. Hindawi 2020-04-19 /pmc/articles/PMC7193272/ /pubmed/32373370 http://dx.doi.org/10.1155/2020/3417910 Text en Copyright © 2020 Ehsan Aghaei Moghadam et al. http://creativecommons.org/licenses/by/4.0/ This is an open access article distributed under the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Aghaei Moghadam, Ehsan
Aslani, Nahid
Mojtabavi, Helia
Larti, Farnoosh
Ghamari, Azin
Ziaee, Vahid
Giant Thrombosis at Left Anterior Descending Artery Aneurysm in a 10-Year Old Boy with Granulomatosis with Polyangiitis
title Giant Thrombosis at Left Anterior Descending Artery Aneurysm in a 10-Year Old Boy with Granulomatosis with Polyangiitis
title_full Giant Thrombosis at Left Anterior Descending Artery Aneurysm in a 10-Year Old Boy with Granulomatosis with Polyangiitis
title_fullStr Giant Thrombosis at Left Anterior Descending Artery Aneurysm in a 10-Year Old Boy with Granulomatosis with Polyangiitis
title_full_unstemmed Giant Thrombosis at Left Anterior Descending Artery Aneurysm in a 10-Year Old Boy with Granulomatosis with Polyangiitis
title_short Giant Thrombosis at Left Anterior Descending Artery Aneurysm in a 10-Year Old Boy with Granulomatosis with Polyangiitis
title_sort giant thrombosis at left anterior descending artery aneurysm in a 10-year old boy with granulomatosis with polyangiitis
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7193272/
https://www.ncbi.nlm.nih.gov/pubmed/32373370
http://dx.doi.org/10.1155/2020/3417910
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