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The nutritional status of people with alkaptonuria: An exploratory analysis suggests a protein/energy dilemma
BACKGROUND: Alkaptonuria (AKU) is a disorder of tyrosine/protein metabolism leading to accumulation of homogentisic acid. Clinical management historically recommended reducing dietary protein intake, especially in childhood, which has since been discredited in the literature. For the first time, ana...
Autores principales: | Judd, Shirley, Khedr, Milad, Milan, Anna M., Davison, Andrew S., Hughes, Andrew T., Needham, Alexander, Psarelli, Eftychia E., Shenkin, Alan, Ranganath, Lakshiminaryan R. |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
John Wiley & Sons, Inc.
2020
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7203650/ https://www.ncbi.nlm.nih.gov/pubmed/32395409 http://dx.doi.org/10.1002/jmd2.12084 |
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