SUN-917 Aggressive De Novo MEN1 Variant in a Child with Metastatic Pancreatic Acth and Crh Co-Secreting Neuroendocrine Tumor: Diagnosis and 10-Year Follow Up

Background: In Multiple Endocrine Neoplasia type 1 (MEN1) only about 2% of pituitary adenomas are ACTH-secreting. Cushing Syndrome due to ectopic ACTH or CRH secretion from neuroendocrine tumors (NETs), carcinoid tumors, or pheochromocytomas is very rare, though patients with MEN1 are at increased r...

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Detalles Bibliográficos
Autores principales: Bompou, Maria Eleni, Flippo, Chelsi L, Zenno, Anna, Keil, Meg F, Stratakis, Constantine A
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Oxford University Press 2020
Materias:
Tumor Biology
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7207494/
http://dx.doi.org/10.1210/jendso/bvaa046.1115

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7207494/
http://dx.doi.org/10.1210/jendso/bvaa046.1115

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