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Choledochal cyst- unusual presentation in the adult phase: Case report

INTRODUCTION: Bile duct cysts are congenital malformations characterized by bile duct dilatation with intra and/or extrahepatic localization. About 80% of cases are diagnosed in childhood, so their presentation in adults is rare and repeatedly associated with complications. PRESENTATION OF CASE: A 3...

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Autores principales: de Albuquerque, Victor Vinicius Monteiro Lins, De Macedo, Frank Pinheiro, Costa, Ketlen G., Rodrigues Seixas Nunes, Zuriel, da Silva Junior, Rubem A.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2020
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7210471/
https://www.ncbi.nlm.nih.gov/pubmed/32387825
http://dx.doi.org/10.1016/j.ijscr.2020.03.014
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author de Albuquerque, Victor Vinicius Monteiro Lins
De Macedo, Frank Pinheiro
Costa, Ketlen G.
Rodrigues Seixas Nunes, Zuriel
da Silva Junior, Rubem A.
author_facet de Albuquerque, Victor Vinicius Monteiro Lins
De Macedo, Frank Pinheiro
Costa, Ketlen G.
Rodrigues Seixas Nunes, Zuriel
da Silva Junior, Rubem A.
author_sort de Albuquerque, Victor Vinicius Monteiro Lins
collection PubMed
description INTRODUCTION: Bile duct cysts are congenital malformations characterized by bile duct dilatation with intra and/or extrahepatic localization. About 80% of cases are diagnosed in childhood, so their presentation in adults is rare and repeatedly associated with complications. PRESENTATION OF CASE: A 38-year-old female patient complained of severe abdominal pain for one month, with no associated cholestatic signs. She underwent abdominal ultrasonography that showed cholelithiasis with extrahepatic bile duct dilatation and underwent cholangiography (MRI), which revealed fusiform dilatation of the proximal portion of the hepatocholedochal, compatible with choledochal cyst. DISCUSSION: In adult patients, clinical manifestations are usually nonspecific, and the diagnosis is established by medical imaging. Magnetic resonance cholangiopancreatography (MRCP) is the gold standard diagnostic today. Treatment with better prognosis consists of total cyst resection with hepaticojejunal anastomosis and intestinal transit reconstruction with Roux-en-Y. CONCLUSION: Bile duct cysts are a rare condition in adults. Currently, increasing access to more accurate medical imaging enables early diagnosis, contributing to the use of therapeutic methods in appropriate time, avoiding development of complications.
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spelling pubmed-72104712020-05-13 Choledochal cyst- unusual presentation in the adult phase: Case report de Albuquerque, Victor Vinicius Monteiro Lins De Macedo, Frank Pinheiro Costa, Ketlen G. Rodrigues Seixas Nunes, Zuriel da Silva Junior, Rubem A. Int J Surg Case Rep Article INTRODUCTION: Bile duct cysts are congenital malformations characterized by bile duct dilatation with intra and/or extrahepatic localization. About 80% of cases are diagnosed in childhood, so their presentation in adults is rare and repeatedly associated with complications. PRESENTATION OF CASE: A 38-year-old female patient complained of severe abdominal pain for one month, with no associated cholestatic signs. She underwent abdominal ultrasonography that showed cholelithiasis with extrahepatic bile duct dilatation and underwent cholangiography (MRI), which revealed fusiform dilatation of the proximal portion of the hepatocholedochal, compatible with choledochal cyst. DISCUSSION: In adult patients, clinical manifestations are usually nonspecific, and the diagnosis is established by medical imaging. Magnetic resonance cholangiopancreatography (MRCP) is the gold standard diagnostic today. Treatment with better prognosis consists of total cyst resection with hepaticojejunal anastomosis and intestinal transit reconstruction with Roux-en-Y. CONCLUSION: Bile duct cysts are a rare condition in adults. Currently, increasing access to more accurate medical imaging enables early diagnosis, contributing to the use of therapeutic methods in appropriate time, avoiding development of complications. Elsevier 2020-04-02 /pmc/articles/PMC7210471/ /pubmed/32387825 http://dx.doi.org/10.1016/j.ijscr.2020.03.014 Text en © 2020 The Author(s) http://creativecommons.org/licenses/by/4.0/ This is an open access article under the CC BY license (http://creativecommons.org/licenses/by/4.0/).
spellingShingle Article
de Albuquerque, Victor Vinicius Monteiro Lins
De Macedo, Frank Pinheiro
Costa, Ketlen G.
Rodrigues Seixas Nunes, Zuriel
da Silva Junior, Rubem A.
Choledochal cyst- unusual presentation in the adult phase: Case report
title Choledochal cyst- unusual presentation in the adult phase: Case report
title_full Choledochal cyst- unusual presentation in the adult phase: Case report
title_fullStr Choledochal cyst- unusual presentation in the adult phase: Case report
title_full_unstemmed Choledochal cyst- unusual presentation in the adult phase: Case report
title_short Choledochal cyst- unusual presentation in the adult phase: Case report
title_sort choledochal cyst- unusual presentation in the adult phase: case report
topic Article
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7210471/
https://www.ncbi.nlm.nih.gov/pubmed/32387825
http://dx.doi.org/10.1016/j.ijscr.2020.03.014
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