Double lung transplantation for end-stage Kartagener syndrome: a case report and literature review

Kartagener syndrome (KS) is an autosomal recessive disorder characterized by situs inversus, paranasal sinusitis and bronchiectasis. We report the successful use of double lung transplant (DLTx) to treat end-stage KS. A 49-year-old Han woman was admitted to Renmin Hospital (Wuhan University, China)...

Descripción completa

Detalles Bibliográficos
Autores principales: Wang, Bo, Zhang, Xinghua, Jiang, Wenyang, Huang, Jie, Chen, Jingyu, Kreisel, Daniel, Danguilan, Jose Luis J., Hsin, Michael, Lin, Huiqing
Formato: Online Artículo Texto
Lenguaje:English
Publicado: AME Publishing Company 2020
Materias:
iMDT Corner
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7212169/
https://www.ncbi.nlm.nih.gov/pubmed/32395296
http://dx.doi.org/10.21037/jtd.2020.02.28
Descripción
Sumario:Kartagener syndrome (KS) is an autosomal recessive disorder characterized by situs inversus, paranasal sinusitis and bronchiectasis. We report the successful use of double lung transplant (DLTx) to treat end-stage KS. A 49-year-old Han woman was admitted to Renmin Hospital (Wuhan University, China) in September 2017 with a ≥15 year history of chronic productive cough that had worsened during the past year. Clinical examination and imaging investigations revealed respiratory failure and situs inversus consistent with KS. The patient was successfully treated with DLTx involving bilateral bronchial anastomoses. DLTx is a feasible treatment option for end-stage KS.

Ejemplares similares