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Kv1.1 Channelopathies: Pathophysiological Mechanisms and Therapeutic Approaches
Kv1.1 belongs to the Shaker subfamily of voltage-gated potassium channels and acts as a critical regulator of neuronal excitability in the central and peripheral nervous systems. KCNA1 is the only gene that has been associated with episodic ataxia type 1 (EA1), an autosomal dominant disorder charact...
Autores principales: | D’Adamo, Maria Cristina, Liantonio, Antonella, Rolland, Jean-Francois, Pessia, Mauro, Imbrici, Paola |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
MDPI
2020
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7215777/ https://www.ncbi.nlm.nih.gov/pubmed/32331416 http://dx.doi.org/10.3390/ijms21082935 |
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