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Skeletal Dysplasias Caused by Sulfation Defects
Proteoglycans (PGs) are macromolecules present on the cell surface and in the extracellular matrix that confer specific mechanical, biochemical, and physical properties to tissues. Sulfate groups present on glycosaminoglycans, linear polysaccharide chains attached to PG core proteins, are fundamenta...
Autores principales: | Paganini, Chiara, Gramegna Tota, Chiara, Superti-Furga, Andrea, Rossi, Antonio |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
MDPI
2020
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7216085/ https://www.ncbi.nlm.nih.gov/pubmed/32295296 http://dx.doi.org/10.3390/ijms21082710 |
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