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Reports of a Conus Cauda Tumor with Holocord Syrinx in an Adolescent Girl

INTRODUCTION: Spinal cord ependymoma seldom presents with holocord syringomyelia in pediatric age-group. Association of ependymoma with a lipoma is also rare. The child presented critically ill with polymicrobial pneumonia, and the neurologic findings were missed until recovery. We report a case hig...

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Detalles Bibliográficos
Autores principales: Sinha, Smriti, Ashwini, Prathibha Shankar, Baba, Pelala Nayan, Shenoy, Rathika Damodar
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Wolters Kluwer - Medknow 2020
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7227757/
https://www.ncbi.nlm.nih.gov/pubmed/32435308
http://dx.doi.org/10.4103/JPN.JPN_96_19
Descripción
Sumario:INTRODUCTION: Spinal cord ependymoma seldom presents with holocord syringomyelia in pediatric age-group. Association of ependymoma with a lipoma is also rare. The child presented critically ill with polymicrobial pneumonia, and the neurologic findings were missed until recovery. We report a case highlighting these findings. CASE REPORT: A 16-year-old adolescent presented critically ill with respiratory failure due to severe pneumonia. Evaluation showed fungal pneumonia with secondary bacterial infection. On recovery, she had nasal regurgitation and required nasogastric tube feeding. Examination showed palatal and left vocal cord palsy. Neuroimaging of brain showed conus cauda tumor with syringobulbia and holocord multiseptate syrinx extending from medulla to filum terminale with lipoma. Histopathology examination showed myxopapillary ependymoma. She improved with excision and postoperative radiotherapy. DISCUSSION: Our case is a rare report of an adolescent girl with conus cauda tumor and holocord syrinx.