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Reports of a Conus Cauda Tumor with Holocord Syrinx in an Adolescent Girl

INTRODUCTION: Spinal cord ependymoma seldom presents with holocord syringomyelia in pediatric age-group. Association of ependymoma with a lipoma is also rare. The child presented critically ill with polymicrobial pneumonia, and the neurologic findings were missed until recovery. We report a case hig...

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Autores principales: Sinha, Smriti, Ashwini, Prathibha Shankar, Baba, Pelala Nayan, Shenoy, Rathika Damodar
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Wolters Kluwer - Medknow 2020
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7227757/
https://www.ncbi.nlm.nih.gov/pubmed/32435308
http://dx.doi.org/10.4103/JPN.JPN_96_19
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author Sinha, Smriti
Ashwini, Prathibha Shankar
Baba, Pelala Nayan
Shenoy, Rathika Damodar
author_facet Sinha, Smriti
Ashwini, Prathibha Shankar
Baba, Pelala Nayan
Shenoy, Rathika Damodar
author_sort Sinha, Smriti
collection PubMed
description INTRODUCTION: Spinal cord ependymoma seldom presents with holocord syringomyelia in pediatric age-group. Association of ependymoma with a lipoma is also rare. The child presented critically ill with polymicrobial pneumonia, and the neurologic findings were missed until recovery. We report a case highlighting these findings. CASE REPORT: A 16-year-old adolescent presented critically ill with respiratory failure due to severe pneumonia. Evaluation showed fungal pneumonia with secondary bacterial infection. On recovery, she had nasal regurgitation and required nasogastric tube feeding. Examination showed palatal and left vocal cord palsy. Neuroimaging of brain showed conus cauda tumor with syringobulbia and holocord multiseptate syrinx extending from medulla to filum terminale with lipoma. Histopathology examination showed myxopapillary ependymoma. She improved with excision and postoperative radiotherapy. DISCUSSION: Our case is a rare report of an adolescent girl with conus cauda tumor and holocord syrinx.
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spelling pubmed-72277572020-05-20 Reports of a Conus Cauda Tumor with Holocord Syrinx in an Adolescent Girl Sinha, Smriti Ashwini, Prathibha Shankar Baba, Pelala Nayan Shenoy, Rathika Damodar J Pediatr Neurosci Case Report INTRODUCTION: Spinal cord ependymoma seldom presents with holocord syringomyelia in pediatric age-group. Association of ependymoma with a lipoma is also rare. The child presented critically ill with polymicrobial pneumonia, and the neurologic findings were missed until recovery. We report a case highlighting these findings. CASE REPORT: A 16-year-old adolescent presented critically ill with respiratory failure due to severe pneumonia. Evaluation showed fungal pneumonia with secondary bacterial infection. On recovery, she had nasal regurgitation and required nasogastric tube feeding. Examination showed palatal and left vocal cord palsy. Neuroimaging of brain showed conus cauda tumor with syringobulbia and holocord multiseptate syrinx extending from medulla to filum terminale with lipoma. Histopathology examination showed myxopapillary ependymoma. She improved with excision and postoperative radiotherapy. DISCUSSION: Our case is a rare report of an adolescent girl with conus cauda tumor and holocord syrinx. Wolters Kluwer - Medknow 2020 2020-03-18 /pmc/articles/PMC7227757/ /pubmed/32435308 http://dx.doi.org/10.4103/JPN.JPN_96_19 Text en Copyright: © 2020 Journal of Pediatric Neurosciences http://creativecommons.org/licenses/by-nc-sa/4.0 This is an open access journal, and articles are distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 4.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as appropriate credit is given and the new creations are licensed under the identical terms.
spellingShingle Case Report
Sinha, Smriti
Ashwini, Prathibha Shankar
Baba, Pelala Nayan
Shenoy, Rathika Damodar
Reports of a Conus Cauda Tumor with Holocord Syrinx in an Adolescent Girl
title Reports of a Conus Cauda Tumor with Holocord Syrinx in an Adolescent Girl
title_full Reports of a Conus Cauda Tumor with Holocord Syrinx in an Adolescent Girl
title_fullStr Reports of a Conus Cauda Tumor with Holocord Syrinx in an Adolescent Girl
title_full_unstemmed Reports of a Conus Cauda Tumor with Holocord Syrinx in an Adolescent Girl
title_short Reports of a Conus Cauda Tumor with Holocord Syrinx in an Adolescent Girl
title_sort reports of a conus cauda tumor with holocord syrinx in an adolescent girl
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7227757/
https://www.ncbi.nlm.nih.gov/pubmed/32435308
http://dx.doi.org/10.4103/JPN.JPN_96_19
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