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Advances in Stem Cell Modeling of Dystrophin-Associated Disease: Implications for the Wider World of Dilated Cardiomyopathy

Familial dilated cardiomyopathy (DCM) is mostly caused by mutations in genes encoding cytoskeletal and sarcomeric proteins. In the pediatric population, DCM is the predominant type of primitive myocardial disease. A severe form of DCM is associated with mutations in the DMD gene encoding dystrophin,...

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Detalles Bibliográficos
Autores principales:	Pioner, Josè Manuel, Fornaro, Alessandra, Coppini, Raffaele, Ceschia, Nicole, Sacconi, Leonardo, Donati, Maria Alice, Favilli, Silvia, Poggesi, Corrado, Olivotto, Iacopo, Ferrantini, Cecilia
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Frontiers Media S.A. 2020
Materias:	Physiology
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC7235370/ https://www.ncbi.nlm.nih.gov/pubmed/32477154 http://dx.doi.org/10.3389/fphys.2020.00368

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